Primary multiple bony epithelioid hemangioendotheliomas mimicking bone metastases: A rare case report
Asian J Surg. 2023 Jul 5:S1015-9584(23)00976-4. doi: 10.1016/j.asjsur.2023.06.118. Online ahead of print.NO ABSTRACTPMID:37419807 | DOI:10.1016/j.asjsur.2023.06.118 (Source: Asian Journal of Surgery)
Source: Asian Journal of Surgery - July 7, 2023 Category: Surgery Authors: Gang Liu Lin Tang Xuanyu Li Dongdong Zhang Source Type: research
Epithelioid Hemangioendothelioma of the Mastoid Bone with Extension of Middle Cranial Fossa: A Case Report
AbstractEpithelioid hemangioendothelioma (EHE) is a rare sarcoma of vascular origin. It is frequently seen in the liver, lungs and bones. Cases with mastoid bone and intracranial extension are rarer. A 40 year old male, presented with a history of progressive headaches and a mass in the postauricular region for a duration of three months. Computer tomography of the temporal bone showed an approximately 40 × 30 mm soft tissue with osteolytic bony changes located in the mastoid bone. Epit helioid hemangioendothelioma is a rare sarcoma of vascular origin. Surgery is the first line of therapy. Prognosis is generally g...
Source: Indian Journal of Otolaryngology and Head and Neck Surgery - July 5, 2023 Category: ENT & OMF Source Type: research
Cancers, Vol. 15, Pages 3304: Prognostic Factors in Epithelioid Hemangioendothelioma: Analysis of a Nationwide Molecularly/Immunohistochemically Confirmed Cohort of 57 Cases
In conclusion, our results demonstrate the aggressive behavior of EHE, emphasize the prognostic value of a previously described risk stratification model and may provide new insights regarding tumor focality, therapeutic strategies and prognosis. (Source: Cancers)
Source: Cancers - June 23, 2023 Category: Cancer & Oncology Authors: Tess Tomassen Yvonne M. H. Versleijen-Jonkers Melissa H. S. Hillebrandt-Roeffen Patricia H. J. Van Cleef Thijs van Dalen Marije E. Weidema Ingrid M. E. Desar Uta Flucke Joost M. van Gorp Tags: Article Source Type: research
Patient with composite haemangioendothelioma containing angiosarcoma-like areas in the setting of congenital lymphoedema mimicking Stewart-Treves syndrome: a case report
Composite haemangioendothelioma is a rare vascular neoplasm with indolent to intermediate malignant potential. Diagnosis of this disease relays on histopathological identification of at least two different mor... (Source: Diagnostic Pathology)
Source: Diagnostic Pathology - June 22, 2023 Category: Pathology Authors: Jan Balko, Andrej Ozaniak, Lenka Krskova, Zuzana Strizova, Robert Lischke and Josef Zamecnik Tags: Case Report Source Type: research
Mesenchymal Neoplasms of the Liver
Mesenchymal neoplasms of the liver can be diagnostically challenging, particularly on core needle biopsies. Here, I discuss recent updates in neoplasms that are specific to the liver (mesenchymal hamartoma, undifferentiated embryonal sarcoma, calcifying nested stromal-epithelial tumor), vascular tumors of the liver (anastomosing hemangioma, hepatic small vessel neoplasm, epithelioid hemangioendothelioma, angiosarcoma), and other tumor types that can occur primarily in the liver (PEComa/angiomyolipoma, inflammatory pseudotumor-like follicular dendritic cell sarcoma, EBV-associated smooth muscle tumor, inflammatory myofibrob...
Source: Surgical Pathology Clinics - June 11, 2023 Category: Pathology Authors: David J. Papke Source Type: research
Incidence, demographics, and survival of malignant hemangioendothelioma in the United States
ConclusionsMalignant hemangioendothelioma is ultra-rare but meaningfully impacts affected patients. These data may provide benchmarks for comparison of new approaches to hemangioendothelioma therapy and highlight poor survival outcomes. (Source: Cancer Medicine)
Source: Cancer Medicine - June 1, 2023 Category: Cancer & Oncology Authors: Kelly G. Paulson,
Vinod Ravi,
Brian P. Rubin,
Min Park,
Elizabeth T. Loggers,
Lee D. Cranmer,
Michael J. Wagner Tags: RESEARCH ARTICLE Source Type: research
Cancers, Vol. 15, Pages 3005: Current Model Systems for Investigating Epithelioid Haemangioendothelioma
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Epithelioid haemangioendothelioma (EHE) is a rare sarcoma of the vascular endothelium with an unpredictable disease course. EHE tumours can remain indolent for long period of time but may suddenly evolve into an aggressive disease with widespread metastases and a poor prognosis. Two mutually exclusive chromosomal translocations define EHE tumours, each involving one of the transcription co-factors TAZ and YAP. The TAZ-CAMTA1 fusion protein results from a t(1;3) translocation and is present in 90% of EHE tumours. The remaining 10% of EHE cases harbour a t(X;11) translocation, resulting in the YAP1-TFE3 (YT) fusion p...
Source: Cancers - May 31, 2023 Category: Cancer & Oncology Authors: Emily Neil Valerie Kouskoff Tags: Review Source Type: research
Intravascular papillary hemangioendothelioma disguised as a peripheral sheath tumor of median nerve at the wrist: a case report and literature review
ConclusionCarpal tunnel syndrome, in exceedingly rare occasions, can result from an IVPH. MRI findings may be confused with more common entities. Histopathological confirmation remains necessary for conclusive diagnosis. (Source: Skeletal Radiology)
Source: Skeletal Radiology - May 25, 2023 Category: Radiology Source Type: research
Characteristic contrast ‑enhanced ultrasound findings of hepatic epithelioid haemangioendothelioma: A case report and literature review
In conclusion, CEUS may be valuable for the diagnosis of HEHE, thereby avoiding the serious consequences of misdiagnosis.PMID:37205916 | PMC:PMC10189842 | DOI:10.3892/ol.2023.13839 (Source: Oncology Letters)
Source: Oncology Letters - May 19, 2023 Category: Cancer & Oncology Authors: Wen Tang Yifan Niu Yang Luo Xiaojuan Ma Source Type: research
Case Report: Kaposiform hemangioendothelioma with PIK3CA mutation successfully treated with sirolimus
Kaposiform hemangioendothelioma (KHE) is an extremely rare, locally aggressive vascular neoplasm. The etiopathogenesis of KHE is still poorly understood. In the present study, we found a new mutation in KHE (c.685delA, p.Thr229fs). The KHE patient with the PIK3CA mutation showed complete regression after sirolimus treatment. We propose that the presence of the PIK3CA mutation in KHE may correlate with good response to sirolimus. (Source: Frontiers in Oncology)
Source: Frontiers in Oncology - May 19, 2023 Category: Cancer & Oncology Source Type: research
Intravascular papillary hemangioendothelioma disguised as a peripheral sheath tumor of median nerve at the wrist: a case report and literature review
ConclusionCarpal tunnel syndrome, in exceedingly rare occasions, can result from an IVPH. MRI findings may be confused with more common entities. Histopathological confirmation remains necessary for conclusive diagnosis. (Source: Skeletal Radiology)
Source: Skeletal Radiology - May 16, 2023 Category: Radiology Source Type: research
Epithelioid hemangioendothelioma as a cause of intestinal intussusception in an adult female patient: case report
CONCLUSIONS: The diagnosis and management process with an appropriate postoperative outcome is described.PMID:37169358 | DOI:10.24875/CIRU.21000708 (Source: Cirugia y Cirujanos)
Source: Cirugia y Cirujanos - May 11, 2023 Category: Surgery Authors: Osama Bahsas-Zaky Jorge R Guill én-Nieto Leonardo Y P Dugarte-Quintero Carlos E G ómez Eduardo E Marquina-Montilla Estrella Uzc átegui-Paz Source Type: research
Epithelioid hemangioendothelioma as a cause of intestinal intussusception in an adult female patient: case report
CONCLUSIONS: The diagnosis and management process with an appropriate postoperative outcome is described.PMID:37169358 | DOI:10.24875/CIRU.21000708 (Source: Cirugia y Cirujanos)
Source: Cirugia y Cirujanos - May 11, 2023 Category: Surgery Authors: Osama Bahsas-Zaky Jorge R Guill én-Nieto Leonardo Y P Dugarte-Quintero Carlos E G ómez Eduardo E Marquina-Montilla Estrella Uzc átegui-Paz Source Type: research
