VEXAS Syndrome: Clinical Case Series From a Canadian Cohort
J Rheumatol. 2024 Mar 15:jrheum.2022-0226. doi: 10.3899/jrheum.2022-0226. Online ahead of print.ABSTRACTVEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic; OMIM #301054) syndrome is an autoinflammatory condition first described in November 2020.1 It is characterized by vacuoles in myeloid and erythroid precursor cells on bone marrow biopsy and caused by a monogenic somatic mutation in the ubiquitin-like modifier activating enzyme 1 (UBA1) gene.1,2.PMID:38490666 | DOI:10.3899/jrheum.2022-0226 (Source: J Rheumatol)
Source: J Rheumatol - March 15, 2024 Category: Rheumatology Authors: Stephen Williams Mohan Stewart Aurore Fifi-Mah Natasha Dehghan Source Type: research
An environmental scan and appraisal of patient online resources for managing rheumatoid arthritis flares
CONCLUSION: There is high variability in the actionability and understandability of RA flare materials online and only 23% of resources were highly recommended by researchers and patient partners.PMID:38490667 | DOI:10.3899/jrheum.2023-1025 (Source: J Rheumatol)
Source: J Rheumatol - March 15, 2024 Category: Rheumatology Authors: Shakeel Subdar Alison M Hoens Krista White Nicole M S Hartfeld Kiran Dhiman Keeva Duffey Claire E Heath Gisele Lamoureux Christine Graveline Eileen Davidson Glen Hazlewood Diane Lacaille Elena Lopatina Megan R W Barber Karen L Then Trafford Crump Saania Z Source Type: research
Comparison Of Attainment And Protective Effects Of Lupus Low Disease Activity State In Patients With Newly Diagnosed Versus Established SLE
CONCLUSION: LLDAS attainment is protective from flare in recent onset SLE. Significant protection from damage accrual was not observed, due to low rates of damage accrual in the first years after SLE diagnosis.PMID:38490668 | DOI:10.3899/jrheum.2023-0900 (Source: J Rheumatol)
Source: J Rheumatol - March 15, 2024 Category: Rheumatology Authors: Vera Golder Rangi Kandane-Rathnayake Worawit Louthrenoo Yi-Hsing Chen Jiacai Cho Aisha Lateef Laniyati Hamijoyo Shue-Fen Luo Yeong-Jian J Wu Sandra V Navarra Leonid Zamora Zhanguo Li Sargunan Sockalingam Yasuhiro Katsumata Masayoshi Harigai Yanjie Hao Zhu Source Type: research
Balancing Honesty and Hope: The Art of Truth-Telling in Medicine
J Rheumatol. 2024 Mar 15:jrheum.2024-0162. doi: 10.3899/jrheum.2024-0162. Online ahead of print.ABSTRACT"Is there any hope I can walk again?"I looked up to see an elderly man lying in the hospital bed struggling to put on his portable hearing aid. I gently removed his blanket to help untangle the wires, exposing his frail body in the process.PMID:38490669 | DOI:10.3899/jrheum.2024-0162 (Source: J Rheumatol)
Source: J Rheumatol - March 15, 2024 Category: Rheumatology Authors: Leonard Kuan-Pei Wang Source Type: research
Cranial Giant Cell Arteritis and Subdural Hematoma
J Rheumatol. 2024 Mar 15:jrheum.2024-0008. doi: 10.3899/jrheum.2024-0008. Online ahead of print.ABSTRACTAlthough it is extremely rare, a few cases of giant cell arteritis (GCA) associated with chronic subdural hematoma (SDH) have been reported.1,2A 68-year-old woman, who had no history of provoking falls, seizures, alcoholism, or coagulopathy, presented with recent onset pulsatile headache, fever, and mild dizziness.PMID:38490670 | DOI:10.3899/jrheum.2024-0008 (Source: J Rheumatol)
Source: J Rheumatol - March 15, 2024 Category: Rheumatology Authors: Hirotaka Yamamoto Yoshinori Taniguchi Source Type: research
