Prenatal diagnosis of submicroscopic chromosomal aberrations in fetuses with congenital cystic adenomatoid malformation by chromosomal microarray analysis
. (Source: Journal of Maternal-Fetal and Neonatal Medicine)
Source: Journal of Maternal-Fetal and Neonatal Medicine - October 4, 2019 Category: Perinatology & Neonatology Authors: Qiong Deng Lihua Huang Juan Liu Fu Fang Zequn Liu Yongling Zhang Fatao Li Can Liao Source Type: research

Whole exome sequencing to uncover genetic variants underlying congenital cystic adenomatoid malformations.
Authors: Tam PK PMID: 31416986 [PubMed - in process] (Source: Hong Kong Medical Journal)
Source: Hong Kong Medical Journal - August 18, 2019 Category: General Medicine Tags: Hong Kong Med J Source Type: research

Congenital Cystic Adenomatoid Malformation Volume Ratio in Prenatal Assessment of Prognosis of Fetal Pulmonary Sequestrations
This study aimed to evaluate the prognosis of pulmonary sequestration (PS) by measuring congenital cystic adenomatoid malformation volume ratio (CVR) value in fetal congenital PS. The fetal CVR in 49 cases of fetal PS diagnosed by prenatal ultrasound in Xiangyang No. 1 People ’s Hospital from March 2010 to June 2017 were measured, and the clinical outcomes were observed. According to the prenatal ultrasound CVR value, 49 fetuses diagnosed with PS were divided into 2 groups: group 1 with CVR≥1.26, and group 2 with CVR
Source: Journal of Huazhong University of Science and Technology -- Medical Sciences -- - July 25, 2019 Category: Research Source Type: research

 A Young Adult with Tracheal Bronchus and Congenital Cystic Adenomatoid Malformation.
 A Young Adult with Tracheal Bronchus and Congenital Cystic Adenomatoid Malformation. J Assoc Physicians India. 2019 Apr;67(4):74-75 Authors: Garg K, Gupta R, Kumar A, Handa U, Saini V PMID: 31309803 [PubMed - in process] (Source: Journal of the Association of Physicians of India)
Source: Journal of the Association of Physicians of India - July 18, 2019 Category: General Medicine Tags: J Assoc Physicians India Source Type: research

Invasive mucinous adenocarcinoma of the lung arising in a type 1 congenital pulmonary airway malformation in a 68-year-old patient: a case report.
Conclusions: Surgical resection should be considered in adults with asymptomatic cysts to prevent malignant transformation. For further analysis, histopathological examination of specimen is essential for a proper diagnosis and eventually further postoperative treatment. PMID: 31262240 [PubMed - as supplied by publisher] (Source: Acta Chirurgica Belgica)
Source: Acta Chirurgica Belgica - July 4, 2019 Category: Surgery Tags: Acta Chir Belg Source Type: research

Fetal Sclerotherapy for Hydropic Congenital Cystic Adenomatoid Malformations of the Lung Refractory to Steroids: A Case Report and Review of the Literature
We describe a case of a large, predominantly microcystic CCAM in a hydropic fetus treated successfully with direct interstitial injection of a sclerosant agent (3% sodium tetradecyl sulfate) at 23+3 weeks gestation, after multiple failed courses of steroids. Elective thoracoscopic right lower lobectomy was performed at 1 year of life and there have been no respiratory or other medical morbidities since. A literature review of fetal lung masses treated with sclerosants antenatally reveals that sclerotherapy may represent a novel treatment option for large hydropic microcystic CCAMs, which are unresponsive to corticosteroids...
Source: Fetal Diagnosis and Therapy - May 21, 2019 Category: Perinatology & Neonatology Source Type: research

[Pulmonary glial heterotopia: Unique lesion in an infant with anencephalic twin].
We report for the first time one case of pulmonary glial heterotopia occured in a one-month baby free from any malformation. She has the particularity of being born from monozygotic monochorionic twin pregnancy where her anencephalic exencephalic sister suffered a medical termination of pregnancy. She presented neonatal respiratory distress, which recurred one month later. Chest X-ray revealed bilateral cystic pulmonary lesions mainly located in the right lung. Given the suspicion of congenital cystic adenomatoid malformation (CCAM), she underwent an upper and a lower right lung lobectomy at four months old. The pathologic...
Source: Annales de Pathologie - December 12, 2018 Category: Pathology Authors: Tournier L, Berrebi D, Peuchmaur M, Bonnard A, Belarbi N, Sibony O, Morcrette G Tags: Ann Pathol Source Type: research

Follow-up of Congenital Lung Malformations (CLM) in a Pediatric tertiary center
Conclusions: Markers of evolution of CLM are difficult to homogenize. Clinical registries may help design more comprehensive care. (Source: European Respiratory Journal)
Source: European Respiratory Journal - November 19, 2018 Category: Respiratory Medicine Authors: Curado, A., Goncalves, C., Saianda, A., Graca, A., Lobo, L., Goncalves, M., Bandeira, T. Tags: Paediatric bronchology Source Type: research

Congenital lobar overinflation in adults - A case series
Conclusion: CLO in adults is rare and is associated with a broad spectrum of symptoms. Precise anamnesis and radiological findings confirm the diagnosis. Surgical resection is the treatment of choice in symptomatic patients. (Source: European Respiratory Journal)
Source: European Respiratory Journal - November 19, 2018 Category: Respiratory Medicine Authors: Sarmand, N., Herth, F., Eichhorn, M., Gompelmann, D. Tags: Clinical Problems Source Type: research

OC23.07: Predictive factors of postnatal outcomes in the fetuses with congenital cystic adenomatoid malformation
Ultrasound in Obstetrics&Gynecology,Volume 52, Issue S1, Page 56-57, October 2018. (Source: Ultrasound in Obstetrics and Gynecology)
Source: Ultrasound in Obstetrics and Gynecology - October 16, 2018 Category: Radiology Authors: S. An, H. Won, M. Lee, J. Shim, P. Lee, A. Kim Source Type: research

Fetal Congenital Peripheral Bronchial Atresia Diagnosed by Magnetic Resonance Imaging: Two Case Reports
We report two cases of peripheral bronchial atresia diagnosed by prenatal ultrasonography (US) and magnetic resonance imaging (MRI). Evaluating an enlarged lung mass that is homogeneously hyperechoic on US and hyperintense on T2-weighted MRI can help in determining whether bronchial atresia is present. Proximal type is suggested when a dilated main bronchus is observed as a tubule structure of an involved lung hilum. In our cases, T2-weighted MRI revealed homogeneously hyperintense lung lesion with decreased signal intensity of adjacent lobe, flattening diaphragm, and mediastinal shift. Dilatation of the main bronchus was ...
Source: American Journal of Perinatology Reports - October 9, 2018 Category: Perinatology & Neonatology Authors: Kozaki, Mitsuru Iraha, Yuko Masamoto, Hitoshi Nitta, Hayase Chinen, Yukiko Kinjo, Tadatsugu Mekaru, Keiko Aoki, Yoichi Tags: Case Report Source Type: research

An autopsy based descriptive study of the spectrum of pulmonary lesions encountered in fetal deaths at a tertiary care center.
Conclusion: Pulmonary pathology is the most common finding in fetal deaths with aspiration pneumonitis being the most common avoidable cause. Accurate fetal autopsy along with clinical data are important in evaluating fetal deaths and can help in reduction of unexplained stillbirths. PMID: 30303136 [PubMed - in process] (Source: Indian Journal of Pathology and Microbiology)
Source: Indian Journal of Pathology and Microbiology - October 1, 2018 Category: Pathology Authors: Neeha S, Kattimani SR, Mahanta AA, Patil AG Tags: Indian J Pathol Microbiol Source Type: research

Predictors of early lobectomy after birth in prenatally diagnosed congenital pulmonary airway malformation
The purpose of this study was to clarify the relationship between congenital pulmonary airway malformation volume ratio (CVR) of bronchial atresia (BA), CVR of congenital cystic adenomatoid malformations (CCAM), and time of surgery after birth. (Source: Journal of Pediatric Surgery)
Source: Journal of Pediatric Surgery - September 20, 2018 Category: Surgery Authors: Yasushi Fuchimoto, Toshihiko Watanabe, Akihiro Fujino, Yutaka Kanamori, Yushi Itoh, Seiji Wada, Haruhiko Sago, Takako Yoshioka Source Type: research

Congenital cystic adenomatoid malformation in adults detected after infection
Respirology Case Reports,Volume 6, Issue 8, November 2018. (Source: Respirology Case Reports)
Source: Respirology Case Reports - September 15, 2018 Category: Respiratory Medicine Authors: Hiroyuki Kagawa , Keisuke Miki , Mari Miki , Koji Urasaki , Seigo Kitada Source Type: research

The usefulness of 3D-CT simulation and intraoperative navigation in pediatric minimally invasive surgery
ConclusionsPreoperative 3D-CT simulation and intraoperative navigation for pediatric minimally invasive surgery were useful and feasible. (Source: Journal of Pediatric Surgery Case Reports)
Source: Journal of Pediatric Surgery Case Reports - July 11, 2018 Category: Surgery Source Type: research

Congenital cystic adenomatoid malformation in adults: Report of a case presenting with a recurrent pneumothorax and a literature review of 60 cases
Publication date: Available online 25 February 2018Source: Respiratory Medicine Case ReportsAuthor(s): Rurika Hamanaka, Hidehiko Yagasaki, Mitsutomo Kohno, Ryota Masuda, Masayuki IwazakiAbstractCongenital cystic adenomatoid malformation (CCAM) is a congenital pulmonary cystic disease that is mostly detected and diagnosed prenatally or during the neonatal period, while rarely being observed in adults. Here, we report an adult case of CCAM that was diagnosed following surgery for a recurrent pneumothorax. We further review 60 case reports on adult CCAM that have been previously published. The patient was a 29-year-old woman ...
Source: Respiratory Medicine Case Reports - July 11, 2018 Category: Respiratory Medicine Source Type: research

Isolated primary agenesis of left lung presenting with recurrent respiratory infections – An uncommon presentation
Publication date: June 2018Source: Egyptian Pediatric Association Gazette, Volume 66, Issue 2Author(s): Mohd Ilyas, Fahad Shafi, Kifayat Hussain Ganaie, Inayat Ellahi, Naseer ChohAbstractThe present article reports a rare case of isolated primary left lung agenesis who presented with the history of recurrent respiratory infections. Lung agenesis is an uncommon entity resulting due to non-proliferation of the lung bud. The agenesis may be complete or partial depending upon the time of proliferative arrest. It may be isolated or associated with organ anomalies. In complete agenesis, there is no development of pulmonary vascu...
Source: Egyptian Pediatric Association Gazette - July 11, 2018 Category: Pediatrics Source Type: research

Congenital cystic adenomatoid malformation: Antenatal ultrasonography features
Publication date: April 2018Source: Medical Journal Armed Forces India, Volume 74, Issue 2Author(s): D.S. Grewal, Arun Kant Singh (Source: Medical Journal Armed Forces India)
Source: Medical Journal Armed Forces India - July 10, 2018 Category: General Medicine Source Type: research

Congenital cystic adenomatoid malformation in adults: Report of a case presenting with a recurrent pneumothorax and a literature review of 60 cases
Publication date: Available online 25 February 2018Source: Respiratory Medicine Case ReportsAuthor(s): Rurika Hamanaka, Hidehiko Yagasaki, Mitsutomo Kohno, Ryota Masuda, Masayuki IwazakiAbstractCongenital cystic adenomatoid malformation (CCAM) is a congenital pulmonary cystic disease that is mostly detected and diagnosed prenatally or during the neonatal period, while rarely being observed in adults. Here, we report an adult case of CCAM that was diagnosed following surgery for a recurrent pneumothorax. We further review 60 case reports on adult CCAM that have been previously published. The patient was a 29-year-old woman ...
Source: Respiratory Medicine Case Reports - July 6, 2018 Category: Respiratory Medicine Source Type: research

Isolated primary agenesis of left lung presenting with recurrent respiratory infections – An uncommon presentation
Publication date: June 2018Source: Egyptian Pediatric Association Gazette, Volume 66, Issue 2Author(s): Mohd Ilyas, Fahad Shafi, Kifayat Hussain Ganaie, Inayat Ellahi, Naseer ChohAbstractThe present article reports a rare case of isolated primary left lung agenesis who presented with the history of recurrent respiratory infections. Lung agenesis is an uncommon entity resulting due to non-proliferation of the lung bud. The agenesis may be complete or partial depending upon the time of proliferative arrest. It may be isolated or associated with organ anomalies. In complete agenesis, there is no development of pulmonary vascu...
Source: Egyptian Pediatric Association Gazette - July 5, 2018 Category: Pediatrics Source Type: research

Congenital cystic adenomatoid malformation: Antenatal ultrasonography features
Publication date: April 2018Source: Medical Journal Armed Forces India, Volume 74, Issue 2Author(s): D.S. Grewal, Arun Kant Singh (Source: Medical Journal Armed Forces India)
Source: Medical Journal Armed Forces India - July 5, 2018 Category: General Medicine Source Type: research

Long-Term Neurodevelopmental and Respiratory Outcome after Intrauterine Therapy for Fetal Thoracic Abnormalities
Discussion: Our results suggest that severe NDI in this specific high-risk cohort occurs in 15%, which is above the range of the incidence of NDI reported in case series treated with other fetal therapies (5 –10%). Large multicenter studies and an international web-based registry are warranted to prospectively gather outcome data at fixed time points.Fetal Diagn Ther (Source: Fetal Diagnosis and Therapy)
Source: Fetal Diagnosis and Therapy - May 7, 2018 Category: Perinatology & Neonatology Source Type: research

Thoracoscopic Resection of Congenital Cystic Adenomatoid Malformation in a Patient With Fused Lung Fissure Using Hookwire
Thoracoscopic resection is being used more commonly for the treatment of congenital cystic adenomatoid malformation in neonates and infants. However, in the rare case of congenital cystic adenomatoid malformation with congenital absence of lung fissure, thoracoscopic lobectomy cannot be performed safely. Moreover, if the lung lesion is deep-seated and cannot be visualized on the pleural surface, wedge resection may result in residual lesion. Here, we reported our approach of thoracoscopic resection under hookwire guidance to tackle this problem. (Source: Innovations: Technology and Techniques in Cardiothoracic and Vascular Surgery)
Source: Innovations: Technology and Techniques in Cardiothoracic and Vascular Surgery - May 1, 2018 Category: Cardiovascular & Thoracic Surgery Tags: Case Reports Source Type: research

Congenital cystic adenomatoid malformation - diagnostic and therapeutic procedure: 8-year experience of one medical centre.
Conclusions: Postnatal management of CCAM depends on the clinical status of the newborn. Newborns without clinical symptoms require radiological diagnostics to confirm the presence of malformation. Surgical treatment is recommended before the age of 10 months. Resection of the malformed lung fragment in patients with CCAM is the first-line treatment. It should be emphasized that despite the tremendous advances in diagnostic imaging, the final diagnosis of CCAM is made based on histopathological findings. PMID: 29681956 [PubMed] (Source: Polish Journal of Cardio-Thoracic Surgery)
Source: Polish Journal of Cardio-Thoracic Surgery - April 24, 2018 Category: Cardiovascular & Thoracic Surgery Tags: Kardiochir Torakochirurgia Pol Source Type: research

Isolated primary agenesis of left lung presenting with recurrent respiratory infections – An uncommon presentation
Publication date: Available online 26 March 2018 Source:Egyptian Pediatric Association Gazette Author(s): Mohd Ilyas, Fahad Shafi, Kifayat Hussain Ganaie, Inayat Ellahi, Naseer Choh The present article reports a rare case of isolated primary left lung agenesis who presented with the history of recurrent respiratory infections. Lung agenesis is an uncommon entity resulting due to non-proliferation of the lung bud. The agenesis may be complete or partial depending upon the time of proliferative arrest. It may be isolated or associated with organ anomalies. In complete agenesis, there is no development of pulmonary vasculatu...
Source: Egyptian Pediatric Association Gazette - March 27, 2018 Category: Pediatrics Source Type: research

Congenital cystic adenomatoid malformation of the lung in adults: report of two cases and review of the literature
We describe two cases of atypical CCAM presenting in adulthood with past history of tuberculosis. To our knowledge only one case of CCAM with tuberculosis has been reported in literature. (Source: Indian Journal of Thoracic and Cardiovascular Surgery)
Source: Indian Journal of Thoracic and Cardiovascular Surgery - February 27, 2018 Category: Cardiovascular & Thoracic Surgery Source Type: research

Congenital cystic adenomatoid malformation in adults: Report of a case presenting with a recurrent pneumothorax and a literature review of 60 cases
Publication date: Available online 25 February 2018 Source:Respiratory Medicine Case Reports Author(s): Rurika Hamanaka Congenital cystic adenomatoid malformation (CCAM) is a congenital pulmonary cystic disease that is mostly detected and diagnosed prenatally or during the neonatal period, while rarely being observed in adults. Here, we report an adult case of CCAM that was diagnosed following surgery for a recurrent pneumothorax. We further review 60 case reports on adult CCAM that have been previously published. The patient was a 29-year-old woman with a severe left pneumothorax. Her computed tomography scan showed the ...
Source: Respiratory Medicine Case Reports - February 25, 2018 Category: Respiratory Medicine Source Type: research

Case of mucinous adenocarcinoma of the lung associated with congenital pulmonary airway malformation in a neonate.
We report an unusual case of a 10-day-old male newborn with a left lower lobe pulmonary cyst who underwent lobectomy, which revealed type II CPAM complicated by multifocal mucinous adenocarcinoma. KRAS sequencing revealed a somatic mutation in Codon12 (GGT → GAT), suggesting the development of a mucinous adenocarcinoma in the background of mucinous metaplasia. Mucinous adenocarcinoma is the most common lung tumor associated with CPAM, but it generally occurs in older children and adults. Further, all cases in the literature are of type I CPAM. This case in a neonate indicates that malignant transformation can occur ve...
Source: Korean Journal of Pediatrics - February 16, 2018 Category: Pediatrics Tags: Korean J Pediatr Source Type: research

Congenital cystic adenomatoid malformation
Publication date: Available online 30 December 2017 Source:International Journal of Pediatrics and Adolescent Medicine Author(s): Kamal M. Alshamiri, Hatem B. Abbod Congenital pulmonary airway malformation of the lung is a rare lesion that commonly affects the lower respiratory tract, which manifests as progressive respiratory distress in the neonatal period. This case is highlighted to raise awareness of the variable evolving morphological and radiological appearance of this entity. (Source: International Journal of Pediatrics and Adolescent Medicine)
Source: International Journal of Pediatrics and Adolescent Medicine - December 31, 2017 Category: Pediatrics Source Type: research

Foregut duplication cyst: a novel computed tomography finding mimicking a small bowel herniaA case report
This report presents a case of mediastinal foregut duplication cyst that mimicked a diaphragmatic small bowel hernia. Patient concern: A 27-month-old girl was first referred for a mediastinal lesion found incidentally on a chest radiograph. At that time, our impression was cystic lung lesion such as congenital pulmonary airway malformation or pulmonary sequestration. At the age 6 years, she presented with recurrent vomiting. The physical examination and laboratory studies were within normal limits. Diagnoses: Chest CT revealed a thin- and smooth-walled cystic mass containing an air-fluid level in the left paravertebr...
Source: Medicine - December 1, 2017 Category: Internal Medicine Tags: Research Article: Clinical Case Report Source Type: research

A “blind” vascular ring in association with congenital cystic adenomatoid malformation: A case report
We report this rare case of CCAM with VR consisting of left aortic arch and right descending aorta with left tracheal compression causing atelectasis. From the findings of this report, early surgical treatment is recommended. Although the prognosis after surgery remained good, second surgery can be avoided if VR was detected early. Rationale: The occurrence of congenital cystic adenomatoid malformation (CCAM) and vascular ring (VR) is extremely rare. Patient concerns: We present a case of left CCAM with VR consisting of a left aortic arch and right descending aorta with left tracheal compression causing atelectasis....
Source: Medicine - December 1, 2017 Category: Internal Medicine Tags: Research Article: Clinical Case Report Source Type: research

Traumatic pulmonary pseudocysts mimicking a congenital malformation of the lung
Publication date: February 2018 Source:Journal of Pediatric Surgery Case Reports, Volume 29 Author(s): Alexander Ngoo, Charlotte Slaney, Bhanu Mariyappara, Harry Stalewski, Daniel Carroll Traumatic Pulmonary Pseudocysts (TPPs) are a rare consequence of thoracic trauma that is seen disproportionately in young adults and paediatric populations. In this case report, we detail a case of a TPP initially misdiagnosed on imaging as a Congenital Cystic Adenomatoid Malformation (CCAM). Conservative management and monitoring for resolution of TPP is highly effective as in most cases it self-resolves without issue or need for interv...
Source: Journal of Pediatric Surgery Case Reports - November 19, 2017 Category: Surgery Source Type: research

OP04.04: Prenatally diagnosed fetal congenital cystic adenomatoid malformation (CCAM) and bronchopulmonary sequestration (BPS) showed excellent survival and prognosis: a 10 ‐year review in a tertiary hospital
(Source: Ultrasound in Obstetrics and Gynecology)
Source: Ultrasound in Obstetrics and Gynecology - September 16, 2017 Category: Radiology Authors: H. Yi, Y. Kim, S. Kim, S. Choi, C. Roh, J. Kim Tags: Abstracts Source Type: research

Congenital cystic adenomatoid malformation – dangers of misdiagnosis: a case report
ConclusionsThe goal of this case report is to firmly express the need for both pediatricians and radiologists to enlarge diagnosis investigations, especially of congenital or constitutional entities in children, as soon as recurrence of respiratory distress and pulmonary infections are manifested. We also emphasize this important entity because of its frequency, to avoid the eventual therapeutic errors. (Source: Journal of Medical Case Reports)
Source: Journal of Medical Case Reports - August 4, 2017 Category: General Medicine Source Type: research

Lack of epithelial PPAR γ causes cystic adenomatoid malformations in mouse fetal lung.
In this study, the function of PPARγ on lung development was investigated. Lung-specific Pparg conditional knockout mice (Pparg(ΔLuEpC)) were developed using Cre-Lox system. Pparg(ΔLuEpC) mice showed abnormal lung development with enlarged airspaces and followed by increase of apoptotic cells at E14.5 to E18.5. Gene analysis revealed that expression of Pmaip1, a gene related to apoptosis, was significantly increased while expression of Retnla, a gene related to anti-apoptosis, was dramatically decreased in the fetal lung (E14.5) of Pparg(ΔLuEpC) mice. In addition, expression of Pthlh, a gene phenoty...
Source: Biochemical and Biophysical Research communications - July 21, 2017 Category: Biochemistry Authors: Kim JH, Yamaori S, Tanabe T, Takagi M, Matsubara T, Okamoto M, Kimura S, Gonzalez FJ Tags: Biochem Biophys Res Commun Source Type: research

Prevalence of prenatally diagnosed congenital cystic adenomatoid malformation among fetuses in China.
Authors: Fan D, Xia Q, Wu S, Liu L, Yu Z, Wang W, Wu S, Guo X, Liu Z Abstract The prevalence of congenital cystic adenomatoid malformation among fetuses still varies in different studies in China. The present meta-analysis was intended to evaluate the pooled prevalence of fetuses in China. Four English (Pubmed, Elsevier Science Direct, Web of Science and the Cochrane Library) and four Chinese (the Chinese Biological Medical Literature database, the Chinese National Knowledge Infrastructure database, VIP database and Wanfang Data) databases were searched from inception to July 2016. Meta-analyses were performed usin...
Source: Oncotarget - June 25, 2017 Category: Cancer & Oncology Tags: Oncotarget Source Type: research

Spontaneous massive hemopneumothorax: Double trouble with a twist
Milta Kuriakose, Arjun Khanna, Deepak TalwarLung India 2017 34(3):283-286Spontaneous hemopneumothorax (SHP) is observed in 3%–7% cases of spontaneous pneumothorax where the tear of an adhesion can lead to bleeding with associated hemothorax. This condition has been reported in patients with hemophilia, sarcoidosis, congenital cystic adenomatoid malformation, systemic lupus erythematosus, etc., Here, we describe an unusual case of acute massive SHP in a 62-year-old male who underwent a percutaneous transluminal coronary angioplasty (PTCA) and presented with worsening dyspnea over the next 3 days. On evaluation...
Source: Lung India - April 28, 2017 Category: Respiratory Medicine Authors: Milta Kuriakose Arjun Khanna Deepak Talwar Source Type: research

Congenital Cystic Adenomatoid Malformation of the Lung: a Case Report and a Brief Review
  Congenital cystic adenomatoid malformation (CCAM) is one of the four types of congenital cystic lesions. The other three are: pulmonary sequestration, bronchogenic cysts, and congenital (Source: Annals of Saudi Medicine)
Source: Annals of Saudi Medicine - April 25, 2017 Category: Journals (General) Tags: ISSUE 4 Source Type: research

Congenital Cystic Adenomatoid Malformation, Type II: A Rare Cause of Haemoptysis.
We describe here the occurrence of congenital cystic adenomatoid malformation of right lung in a 12-year-old girl presenting with haemoptysis and hypovolaemic shock. She underwent right middle lobectomy; and histopathological examination confirmed the diagnosis. She has been doing well on follow-up. PMID: 28393565 [PubMed - as supplied by publisher] (Source: Indian Journal of Chest Diseases and Allied Sciences)
Source: Indian Journal of Chest Diseases and Allied Sciences - April 12, 2017 Category: Respiratory Medicine Tags: Indian J Chest Dis Allied Sci Source Type: research

Congenital cystic adenomatoid malformation: Antenatal ultrasonography features
Publication date: Available online 7 April 2017 Source:Medical Journal Armed Forces India Author(s): D.S. Grewal, Arun Kant Singh (Source: Medical Journal Armed Forces India)
Source: Medical Journal Armed Forces India - April 11, 2017 Category: Journals (General) Source Type: research

First experience with biodegradable airway stents in children – Case report
Publication date: Available online 8 April 2017 Source:Pediatria Polska Author(s): Andrzej Zając, Mirosław Krysta, Przemysław Tomasik, Wojciech Górecki Airway malacia is the most common cause of tracheobronchial obstruction in children. It can be congenital or acquired. Aortopexy and surgical relief of external compression are main therapeutical options. An alternative for surgical approach can be metallic airway stents, but usually they are not considered as a first choice, because of relatively high risk of complications. Moreover, metallic airway stents are permanent, so they have limited usage in growing bro...
Source: Pediatria Polska - April 11, 2017 Category: Pediatrics Source Type: research

Trisomy 13 with prenatally diagnosed congenital cystic adenomatoid malformation and hernia of the umbilical cord: A case report.
Authors: Nakamura K, Aoki S, Ishihara T, Nakayama K, Kanasaki H, Kyo S PMID: 28285557 [PubMed - as supplied by publisher] (Source: Journal of Obstetrics and Gynaecology)
Source: Journal of Obstetrics and Gynaecology - March 15, 2017 Category: OBGYN Tags: J Obstet Gynaecol Source Type: research

Successfully treated congenital cystic adenomatoid malformation by open fetal surgery: A care-compliant case report of a 5-year follow-up and review of the literature
Conclusion: We present one case of CCAM which was cured by open fetal surgery and continued to do well at follow-up of 5 years. The success of treatment provided preliminary experience for further carrying out such interventions in China. (Source: Medicine)
Source: Medicine - January 1, 2017 Category: Internal Medicine Tags: Research Article: Clinical Case Report Source Type: research

Perpetual dilemma: Pleural or parenchymal/congenital or acquired solitary cystic lesion with fluid level
Deepak Talwar, Onkar Jha, Rahul Kumar Sharma, Rajat SaxenaLung India 2017 34(1):88-91 Congenital cystic adenomatoid malformations (CCAMs) are rare congenital, nonhereditary developmental anomalies of the lung with unknown etiology. CCAM is predominantly a disorder of infancy with the majority of the cases being diagnosed within the first 2 years of life. When CCAM presents in adults, it represents a diagnostic dilemma and requires careful evaluation. We here report a case of large solitary congenital pulmonary cystic adenomatoid malformation with infection and hemorrhage, which was diagnosed as encysted hydropneumothorax ...
Source: Lung India - December 30, 2016 Category: Respiratory Medicine Authors: Deepak Talwar Onkar Jha Rahul Kumar Sharma Rajat Saxena Source Type: research

Prenatally diagnosed congenital cystic adenomatoid malformation (CCAM) and pulmonary sequestration (PS): Long-term follow-up of 119 cases
Conclusion: Conservative management of asymptomatic CCAM and PS is a reasonable option during the paediatric period.The risk of recurrent infection is
Source: European Respiratory Journal - November 8, 2016 Category: Respiratory Medicine Authors: Cook, J., Chitty, L. S., De Coppi, P., Ashworth, M., Wallis, C. Tags: 7.7 Paediatric Bronchology Source Type: research

Cystic adenomatoid malformation of the lung in adult patients: Clinicoradiological features and surgical management
Conclusions: CCAM is rare in adults. Although adult patients may present with nonspecific thoracic symptoms, it is not unusual that this entity is incidentally diagnosed on routine chest imaging. Most adult CCAM of the lung can be safely treated with minimally invasive techniques, but conservative management is another reasonable option in certain clinical scenarios. (Source: European Respiratory Journal)
Source: European Respiratory Journal - November 8, 2016 Category: Respiratory Medicine Authors: Arrieta Narvaez, P. L., Gorospe Sarasua, L., Munoz Molina, G., Mirambeaux Villalona, R. M. Tags: 1.3 Imaging Source Type: research

Congenital cystic adenomatoid malformation associated with esophageal duplication cyst
Congenital cystic adenomatoid malformation (CCAM) of the lung is rare and is characterized by an excessive overgrowth of the terminal bronchioles.1 Patients with CCAM may present either in the newborn period with progressive respiratory distress, or rarely in older children and adults with recurrent pulmonary infections. Intrathoracic foregut duplication cysts are also rare, and depending on their size, may be asymptomatic and discovered incidentally, or may present with a variety of symptoms, most commonly airway or esophageal obstruction.2 The coexistence of both CCAM and esophageal duplication cyst (EDC) is extremely ra...
Source: Annals of Saudi Medicine - October 3, 2016 Category: Journals (General) Tags: ISSUE 1 Source Type: research

Congenital cystic adenomatoid malformation of the lung (CCAM), a retrospective clinical audit and literature review in a tertiary centre in Scotland over a period of 14 years.
Authors: Shamas AG, Bohara K Abstract This work was a retrospective audit of CCAM - 1994 to 2008. A total of 26 cases were identified. Mean gestational age at diagnosis was 20 weeks. All were unilateral and had serial scans. In 31% the lesion resolved, 8% decreased, 42% were unchanged and 4% increased in size. Only one foetus developed hydrops. All were born alive. Of 8 foetuses where the CCAM was thought to have resolved, 6 had persistent lesions (overall sensitivity and PPV of US 64% and 69%, respectively). Computerised tomography performed better than chest X-ray in detecting lesions postnatally (sensitivity 100...
Source: Journal of Obstetrics and Gynaecology - September 27, 2016 Category: OBGYN Tags: J Obstet Gynaecol Source Type: research

P07.03: Prenatal ultrasound predictor factors in congenital cystic adenomatoid malformation
(Source: Ultrasound in Obstetrics and Gynecology)
Source: Ultrasound in Obstetrics and Gynecology - September 8, 2016 Category: Radiology Authors: A. Abascal Saiz, E. Antolin, A. Mateos, R. Rodriguez, J. Encinas, F. Lopez, H. Beatriz, L. Sotillo, J. Bartha Tags: Abstracts Source Type: research