Congenital Cystic Adenomatous Malformation (CCAM) Research This is an RSS file. You can use it to subscribe to this data in your favourite RSS reader or to display this data on your own website or blog.

Isolated primary agenesis of left lung presenting with recurrent respiratory infections – An uncommon presentation
Publication date: June 2018Source: Egyptian Pediatric Association Gazette, Volume 66, Issue 2Author(s): Mohd Ilyas, Fahad Shafi, Kifayat Hussain Ganaie, Inayat Ellahi, Naseer ChohAbstractThe present article reports a rare case of isolated primary left lung agenesis who presented with the history of recurrent respiratory infections. Lung agenesis is an uncommon entity resulting due to non-proliferation of the lung bud. The agenesis may be complete or partial depending upon the time of proliferative arrest. It may be isolated or associated with organ anomalies. In complete agenesis, there is no development of pulmonary vascu...
Source: Egyptian Pediatric Association Gazette - July 10, 2018 Category: Pediatrics Source Type: research

Congenital cystic adenomatoid malformation: Antenatal ultrasonography features
Publication date: April 2018Source: Medical Journal Armed Forces India, Volume 74, Issue 2Author(s): D.S. Grewal, Arun Kant Singh (Source: Medical Journal Armed Forces India)
Source: Medical Journal Armed Forces India - July 10, 2018 Category: General Medicine Source Type: research

Congenital cystic adenomatoid malformation in adults: Report of a case presenting with a recurrent pneumothorax and a literature review of 60 cases
Publication date: Available online 25 February 2018Source: Respiratory Medicine Case ReportsAuthor(s): Rurika Hamanaka, Hidehiko Yagasaki, Mitsutomo Kohno, Ryota Masuda, Masayuki IwazakiAbstractCongenital cystic adenomatoid malformation (CCAM) is a congenital pulmonary cystic disease that is mostly detected and diagnosed prenatally or during the neonatal period, while rarely being observed in adults. Here, we report an adult case of CCAM that was diagnosed following surgery for a recurrent pneumothorax. We further review 60 case reports on adult CCAM that have been previously published. The patient was a 29-year-old woman ...
Source: Respiratory Medicine Case Reports - July 5, 2018 Category: Respiratory Medicine Source Type: research

Isolated primary agenesis of left lung presenting with recurrent respiratory infections – An uncommon presentation
Publication date: June 2018Source: Egyptian Pediatric Association Gazette, Volume 66, Issue 2Author(s): Mohd Ilyas, Fahad Shafi, Kifayat Hussain Ganaie, Inayat Ellahi, Naseer ChohAbstractThe present article reports a rare case of isolated primary left lung agenesis who presented with the history of recurrent respiratory infections. Lung agenesis is an uncommon entity resulting due to non-proliferation of the lung bud. The agenesis may be complete or partial depending upon the time of proliferative arrest. It may be isolated or associated with organ anomalies. In complete agenesis, there is no development of pulmonary vascu...
Source: Egyptian Pediatric Association Gazette - July 5, 2018 Category: Pediatrics Source Type: research

Congenital cystic adenomatoid malformation: Antenatal ultrasonography features
Publication date: April 2018Source: Medical Journal Armed Forces India, Volume 74, Issue 2Author(s): D.S. Grewal, Arun Kant Singh (Source: Medical Journal Armed Forces India)
Source: Medical Journal Armed Forces India - July 5, 2018 Category: General Medicine Source Type: research

Long-Term Neurodevelopmental and Respiratory Outcome after Intrauterine Therapy for Fetal Thoracic Abnormalities
Discussion: Our results suggest that severe NDI in this specific high-risk cohort occurs in 15%, which is above the range of the incidence of NDI reported in case series treated with other fetal therapies (5 –10%). Large multicenter studies and an international web-based registry are warranted to prospectively gather outcome data at fixed time points.Fetal Diagn Ther (Source: Fetal Diagnosis and Therapy)
Source: Fetal Diagnosis and Therapy - May 7, 2018 Category: Perinatology & Neonatology Source Type: research

Thoracoscopic Resection of Congenital Cystic Adenomatoid Malformation in a Patient With Fused Lung Fissure Using Hookwire
Thoracoscopic resection is being used more commonly for the treatment of congenital cystic adenomatoid malformation in neonates and infants. However, in the rare case of congenital cystic adenomatoid malformation with congenital absence of lung fissure, thoracoscopic lobectomy cannot be performed safely. Moreover, if the lung lesion is deep-seated and cannot be visualized on the pleural surface, wedge resection may result in residual lesion. Here, we reported our approach of thoracoscopic resection under hookwire guidance to tackle this problem. (Source: Innovations: Technology and Techniques in Cardiothoracic and Vascular Surgery)
Source: Innovations: Technology and Techniques in Cardiothoracic and Vascular Surgery - May 1, 2018 Category: Cardiovascular & Thoracic Surgery Tags: Case Reports Source Type: research

Congenital cystic adenomatoid malformation - diagnostic and therapeutic procedure: 8-year experience of one medical centre.
Conclusions: Postnatal management of CCAM depends on the clinical status of the newborn. Newborns without clinical symptoms require radiological diagnostics to confirm the presence of malformation. Surgical treatment is recommended before the age of 10 months. Resection of the malformed lung fragment in patients with CCAM is the first-line treatment. It should be emphasized that despite the tremendous advances in diagnostic imaging, the final diagnosis of CCAM is made based on histopathological findings. PMID: 29681956 [PubMed] (Source: Polish Journal of Cardio-Thoracic Surgery)
Source: Polish Journal of Cardio-Thoracic Surgery - April 24, 2018 Category: Cardiovascular & Thoracic Surgery Tags: Kardiochir Torakochirurgia Pol Source Type: research

Isolated primary agenesis of left lung presenting with recurrent respiratory infections – An uncommon presentation
Publication date: Available online 26 March 2018 Source:Egyptian Pediatric Association Gazette Author(s): Mohd Ilyas, Fahad Shafi, Kifayat Hussain Ganaie, Inayat Ellahi, Naseer Choh The present article reports a rare case of isolated primary left lung agenesis who presented with the history of recurrent respiratory infections. Lung agenesis is an uncommon entity resulting due to non-proliferation of the lung bud. The agenesis may be complete or partial depending upon the time of proliferative arrest. It may be isolated or associated with organ anomalies. In complete agenesis, there is no development of pulmonary vas...
Source: Egyptian Pediatric Association Gazette - March 27, 2018 Category: Pediatrics Source Type: research

Congenital cystic adenomatoid malformation of the lung in adults: report of two cases and review of the literature
We describe two cases of atypical CCAM presenting in adulthood with past history of tuberculosis. To our knowledge only one case of CCAM with tuberculosis has been reported in literature. (Source: Indian Journal of Thoracic and Cardiovascular Surgery)
Source: Indian Journal of Thoracic and Cardiovascular Surgery - February 27, 2018 Category: Cardiovascular & Thoracic Surgery Source Type: research

Congenital cystic adenomatoid malformation in adults: Report of a case presenting with a recurrent pneumothorax and a literature review of 60 cases
Publication date: Available online 25 February 2018 Source:Respiratory Medicine Case Reports Author(s): Rurika Hamanaka Congenital cystic adenomatoid malformation (CCAM) is a congenital pulmonary cystic disease that is mostly detected and diagnosed prenatally or during the neonatal period, while rarely being observed in adults. Here, we report an adult case of CCAM that was diagnosed following surgery for a recurrent pneumothorax. We further review 60 case reports on adult CCAM that have been previously published. The patient was a 29-year-old woman with a severe left pneumothorax. Her computed tomography scan showed th...
Source: Respiratory Medicine Case Reports - February 25, 2018 Category: Respiratory Medicine Source Type: research

Case of mucinous adenocarcinoma of the lung associated with congenital pulmonary airway malformation in a neonate.
We report an unusual case of a 10-day-old male newborn with a left lower lobe pulmonary cyst who underwent lobectomy, which revealed type II CPAM complicated by multifocal mucinous adenocarcinoma. KRAS sequencing revealed a somatic mutation in Codon12 (GGT → GAT), suggesting the development of a mucinous adenocarcinoma in the background of mucinous metaplasia. Mucinous adenocarcinoma is the most common lung tumor associated with CPAM, but it generally occurs in older children and adults. Further, all cases in the literature are of type I CPAM. This case in a neonate indicates that malignant transformation can occur very ...
Source: Korean Journal of Pediatrics - February 16, 2018 Category: Pediatrics Tags: Korean J Pediatr Source Type: research

Congenital cystic adenomatoid malformation
Publication date: Available online 30 December 2017 Source:International Journal of Pediatrics and Adolescent Medicine Author(s): Kamal M. Alshamiri, Hatem B. Abbod Congenital pulmonary airway malformation of the lung is a rare lesion that commonly affects the lower respiratory tract, which manifests as progressive respiratory distress in the neonatal period. This case is highlighted to raise awareness of the variable evolving morphological and radiological appearance of this entity. (Source: International Journal of Pediatrics and Adolescent Medicine)
Source: International Journal of Pediatrics and Adolescent Medicine - December 31, 2017 Category: Pediatrics Source Type: research

A “blind” vascular ring in association with congenital cystic adenomatoid malformation: A case report
We report this rare case of CCAM with VR consisting of left aortic arch and right descending aorta with left tracheal compression causing atelectasis. From the findings of this report, early surgical treatment is recommended. Although the prognosis after surgery remained good, second surgery can be avoided if VR was detected early. Rationale: The occurrence of congenital cystic adenomatoid malformation (CCAM) and vascular ring (VR) is extremely rare. Patient concerns: We present a case of left CCAM with VR consisting of a left aortic arch and right descending aorta with left tracheal compression causing atelectasis....
Source: Medicine - December 1, 2017 Category: Internal Medicine Tags: Research Article: Clinical Case Report Source Type: research

Foregut duplication cyst: a novel computed tomography finding mimicking a small bowel herniaA case report
This report presents a case of mediastinal foregut duplication cyst that mimicked a diaphragmatic small bowel hernia. Patient concern: A 27-month-old girl was first referred for a mediastinal lesion found incidentally on a chest radiograph. At that time, our impression was cystic lung lesion such as congenital pulmonary airway malformation or pulmonary sequestration. At the age 6 years, she presented with recurrent vomiting. The physical examination and laboratory studies were within normal limits. Diagnoses: Chest CT revealed a thin- and smooth-walled cystic mass containing an air-fluid level in the left paravertebr...
Source: Medicine - December 1, 2017 Category: Internal Medicine Tags: Research Article: Clinical Case Report Source Type: research