Hepatic Manifestations of Cystic Fibrosis.
Hepatic Manifestations of Cystic Fibrosis.
Clin Liver Dis. 2019 May;23(2):263-277
Authors: Sakiani S, Kleiner DE, Heller T, Koh C
Abstract
Cystic fibrosis liver disease (CFLD) remains the third leading cause of death in patients with cystic fibrosis. Although most patients with CFLD present in childhood, recent studies suggest a second wave of liver disease in adulthood. There are no clear guidelines for diagnosing CFLD. Treatment options for CFLD remain limited, and while UDCA is widely used, its long-term benefit is unclear. Those who develop hepatic decompensation or uncontrolled variceal bleeding may benefit from liver transplant, either alone, or in combination with lung transplant.
PMID: 30947876 [PubMed - in process]
Source: Clinical Lung Cancer - Category: Cancer & Oncology Authors: Sakiani S, Kleiner DE, Heller T, Koh C Tags: Clin Liver Dis Source Type: research
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