Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

Camptodactyly-arthropathy-coxa vara-pericarditis syndrome and an unusual association with mitral stenosis
CONCLUSIONS: The main defect is the proteoglycan 4 protein which acts like a lubricant in articular and visceral surfaces. Therefore, the leading clinical feature is arthropathy. Cardiac involvement other than clinically mild pericarditis is not usually expected. Three types of proteoglycans (decorin, biglycan, and versican) are present in the mitral valve. This could be the reason of mitral valve involvement in rare cases as like ours. It is important that these patients undergo echocardiographic examination regularly.PMID:38523390 | DOI:10.24953/turkjped.2023.647 (Source: The Turkish Journal of Pediatrics)
Source: The Turkish Journal of Pediatrics - March 25, 2024 Category: Pediatrics Authors: Duygu Şimşekli Canan Ayabakan Ayla Oktay Ahmet Arnaz Vusal Mahmudov Yusuf Kenan Yal çınbaş Source Type: research

INFLA-score: a new diagnostic paradigm to identify pericarditis
CONCLUSIONS: INFLA-score is a useful diagnostic tool to assess the probability of pericarditis, with a strong prognostic value for further recurrences, outperforming CRP.PMID:38521501 | DOI:10.1016/j.hjc.2024.03.010 (Source: Hellenic Journal of Cardiology)
Source: Hellenic Journal of Cardiology - March 23, 2024 Category: Cardiology Authors: Alessandro Andreis Andrea Solano Marco Balducci Cristina Picollo Margherita Ghigliotti Mario Giordano Alessandra Agosti Valentino Collini Matteo Anselmino Gaetano Maria De Ferrari Mauro Rinaldi Gianluca Alunni Massimo Imazio Source Type: research