Major aortopulmonary collateral arteries

Major aortopulmonary collateral arteries Major aortopulmonary collateral arteries (MAPCA) occur in cyanotic congenital heart diseases with decreased pulmonary blood flow (tetralogy of Fallot like physiology). They are a natural protective mechanism to improve pulmonary blood flow. MAPCAs are more likely to occur in pulmonary atresia than in simple tetralogy of Fallot. MAPCAs can also occur in conditions other than the typical pulmonary atresia with ventricular septal defect. In a retrospective review of such cases, 33 had single ventricle anatomy while the rest had two ventricle anatomy. Among those with single ventricle, 15 had unbalanced complete atrioventricular canal, 6 had pulmonary atresia with intact ventricular septum and 12 with other forms of single ventricular physiology. Among the 17 patients with MAPCAs and two ventricle, 5 had complete atrioventricular canal, 4 had corrected transposition, 3 had double outlet right ventricle, 3 had scimitar syndrome and 2 had complex D-transposition of great arteries [1]. A study from Stanford University reported on all infants undergoing first cardiac surgery for tetralogy of Fallot/MAPCAs from 2001 to 2019 [2]. 1068 MAPCAs were noted in 276 patients. 55% had incompletely arborizing pulmonary arteries, 17% had normally arborizing pulmonary arteries and 16% had absent pulmonary arteries. Unilateral MAPCAs were noted in 11%. Each of the 18 pulmonary segments could be supplied either by a MAPCA, central pulmonary artery or both. B...
Source: Cardiophile MD - Category: Cardiology Authors: Tags: Cardiology Source Type: blogs