Pulmonary arterial hypertension in the setting of scleroderma is different than in the setting of lupus: A review

Pulmonary hypertension (PH) is a clinical syndrome that is subdivided into five groups per the World Health Organization (WHO) classification, based largely on hemodynamic and pathophysiologic criteria. WHO Group 1  PH, termed pulmonary arterial hypertension (PAH), is a clinically progressive disease that can eventually lead to right heart failure and death, and it is hemodynamically characterized by pre-capillary PH and increased pulmonary vascular resistance in the absence of elevated left ventricular filli ng pressures.

Source: Respiratory Medicine - November 28, 2017 Category: Respiratory Medicine Authors: Isabel S. Bazan, Kofi A. Mensah, Anastasiia A. Rudkovskaia, Percy K. Adonteng-Boateng, Erica L. Herzog, Lenore Buckley, Wassim H. Fares Tags: Review article Source Type: research