Electromyographic Features in a Chinese Cohort With Hereditary Skeletal Muscle Channelopathies

Conclusions: Myotonic discharges help to discriminate chloride and sodium from other channelopathies. Early decline and low baseline compound motor action potential amplitude in long exercise test are significant in patients with potassium voltage-gated channel subfamily J member 2 and calcium voltage-gated channel subunit alpha 1S mutations, respectively. Electromyographic patterns in the electromyography study and exercise test may help in better providing the comprehensive picture for patients with primary skeletal muscle channelopathies.
Source: Journal of Clinical Neurophysiology - Category: Neurology Tags: Original Research Source Type: research