Outcomes of long term treatments of type I hereditary angioedema in a Turkish family

Conclusion: Patients with C1-INH hereditary angioedema may be misdiagnosed as having familial Mediterranean fever in regions where the disorder is endemic. Medical history, suspicion of hereditary angioedema and laboratory evaluations of patients and their family members lead the correct diagnoses of hereditary angioedema. Danazol and C1 replacement treatments provide significant reduction in hereditary angioedema attacks.
Source: Anais Brasileiros de Dermatologia - Category: Dermatology Source Type: research