Primary Sjögren's syndrome presenting with multiple aneurysmal dilatation of cerebral arteries and causing repetitive intracranial hemorrhage

Sjögren's syndrome (SS) is characterized by mononuclear infiltration and destruction of salivary and lachrymal glands leading to xerostomia and xerophthalmia [1]. This syndrome is classified as primary SS in the absence of other autoimmune diseases, and as secondary SS when it is associated with other autoimmune diseases such as rheumatoid arthritis, scleroderma, and systemic lupus erythematosus. The incidence of stroke among patients with SS is 2% and SS is even more rarely complicated with cerebral artery lesions [2].

Source: Journal of the Neurological Sciences - April 18, 2016 Category: Neurology Authors: Teppei Komatsu, Hidetaka Mitsumura, Ichiro Yuki, Yasuyuki Iguchi Tags: Letter to the Editor Source Type: research