Rare presentation of multiple thromboses in Erdheim-Chester disease: a case-based review

CONCLUSION: We report a rare case of multiple thromboses, embolism, and multiple organ involvement as the main presentation of ECD, suggesting that ECD should be considered in patients presenting with multiple thromboses associated with multisystem damage. We successfully treated our patient with glucocorticoids and interleukin-6 antagonist. This patient's response to treatment suggests that hormone therapy and cytokine/chemokine therapy may be a potential novel treatment for patients with ECD without gene mutations.PMID:35687294 | DOI:10.1007/s12185-022-03393-x

Source: International Journal of Hematology - June 10, 2022 Category: Hematology Authors: Yongchang Liu Changpin Huang Xiaohu Meng Xin Fang Xupin Xie Changrong Wang Meiyun Wang Source Type: research