QRS Duration After Pulmonary Valve Replacement in Adults with Repaired Tetralogy of Fallot: Association with Ventricular Arrhythmia and Correlation with Right Ventricular Size
AbstractThe aim of this study is to analyze the relationship between QRS duration after pulmonary valve replacement (PVR) and ventricular arrhythmias (VA) in patients with repaired tetralogy of Fallot (ToF). ToF patients may face complications such as heart failure and VA after primary repair, often mitigated by PVR. Prior studies have shown a decrease in QRS duration and right ventricular (RV) size following PVR. It remains unclear whether a lack of QRS duration reduction identifies patients at risk of VA. We retrospectively identified adult patients with repaired ToF who underwent surgical or transcatheter PVR. EKG data ...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Establishing Carotid Seldinger as Routine Access in Infants; Planning, Performance, and Follow-Up Protocols
AbstractPercutaneous carotid access (PCA) in infants has been reported in small multicenter cohorts, case reports and wider studies over the last 20  years. Compare outcomes after implementation of a systematic approach to PCA in a single center including an imaging follow-up protocol. Retrospective case–control study of PCA at Children’s Hospital Colorado was performed from January 2013 to December 2022. Seventy-four patients underwent 82 PCAs for cardiac catheterization. The median age (range) was 14 days (1–359), and weight was 3.25-kg (1.9–7.9). Median sheath size was 4-Fr (3.3–6). Seventy-seven interventio...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Outcomes in Primary Repair of Truncus Arteriosus with Significant Truncal Valve Insufficiency: A Systematic Review and Meta-analysis
AbstractData regarding the effect of significant TVI on outcomes after truncus arteriosus (TA) repair are limited. The aim of this meta-analysis was to summarize outcomes among patients aged  ≤ 24 months undergoing TA repair with at least moderate TVI. A systematic literature search was conducted in PubMed, Scopus, and CINAHL Complete from database inception through June 1, 2022. Studies reporting outcomes of TA repair in patients with moderate or greater TVI were included. Studi es reporting outcomes only for patients aged >  24 months were excluded. The primary outcome was overall mortality, and secondary o...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Characterizing the Use of Exercise Testing in Repaired Tetralogy of Fallot Patients: A Multi-Institutional Survey
AbstractCardiopulmonary exercise testing (CPET) is an important tool used in the management of patients with congenital heart disease. However, there are no clear guidelines for its use in specific populations, such as repaired Tetralogy of Fallot (rTOF). We sought to characterize current practice patterns and attitudes regarding exercise testing in the rTOF population using an online survey distributed to pediatric cardiologists. Analyses were performed using qualitative statistics, Wilcoxon rank-sum, Kruskal –Wallis test, and chi-squared analysis. 103 clinicians completed the survey with 83% routinely sending symptomat...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Mid-Systolic Notching of the Pulmonary Valve Doppler Signal is Highly Associated with Pulmonary Hypertension
AbstractMid-systolic notching (MSN) of the pulmonary valve Doppler signal represents a reflected systolic pressure wave from the pulmonary vasculature and is often seen in pulmonary hypertension (PH). We hypothesize that MSN is associated with a higher pulmonary vascular resistance (PVR) and mean pulmonary artery pressure (mPAP), and a diagnosis of PH in pediatric patients. This was a retrospective study of patients  ≤ 18 years who had an echocardiogram obtained ≤ 30 days before catheterization for suspected PH. MSN was defined as an indentation in the initial two thirds of the systolic Doppler signal. PH was...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Combined Atrial Volume is Associated with Significant Atrial Arrhythmias in Total Cavopulmonary Connection Fontan Patients
AbstractAtrial arrhythmias are a common late manifestation after Fontan palliation and are known to contribute to significant morbidity and mortality. Atrial volume by cardiac magnetic resonance imaging has been increasingly used in patients with congenital heart disease with no reports in those with Fontan palliation. In acquired heart disease, left atrial volume has been shown to be a strong predictor of outcomes of sustained atrial arrhythmias, including recurrence of atrial fibrillation. We hypothesized that combined atrial volume (CAV) in patients with total cavopulmonary connection (TCPC) Fontan palliation may be ass...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

The Use of Virtual Reality Learning on Transition Education in Adolescents with Congenital Heart Disease
This study demonstrates that adolescents enjoyed using SVH and found it helpful. Clinical implementation shows promise as a plausible adjunct t ool for transition education. (Source: Pediatric Cardiology)
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

The Effects of Cardiac Implantable Electronic Device Personal Protective Equipment Use in Patients with Pediatric and Adult Congenital Heart Disease
AbstractPediatric and adult congenital heart disease (ACHD) patients encounter physical and emotional barriers. Cardiac implantable electronic devices (CIEDs), including pacemakers and implantable cardiac defibrillators (ICD) often compound these issues. Patient fear associated with damaging the CIED system can lead to avoidance of physical activity and reduced quality of life (QOL). CIED personal protective equipment (PPE) is a potential treatment for decreasing this fear. We sought to determine the effects of CIED PPE use in the pediatric and ACHD population. Patients 5 years or older with a CIED at a single pediatric an...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

A Novel Approach to Fetal ECG Extraction Using Temporal Convolutional Encoder –Decoder Network (TCED-Net)
AbstractTo extract weak fetal ECG signals from the mixed ECG signal on the mother's abdominal wall, providing a basis for accurately estimating fetal heart rate and analyzing fetal ECG morphology. First, based on the relationship between the maternal chest ECG signal and the maternal ECG component in the abdominal signal, the temporal convolutional encoder-decoder network (TCED-Net) model is trained to fit the nonlinear transmission of the maternal ECG signal from the chest to the abdominal wall. Then, the maternal chest ECG signal is nonlinearly transformed to estimate the maternal ECG component in the abdominal mixed sig...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Open Field Exercise Testing in Pediatric Congenital Heart Disease Patients: A Subsumption of Cardiovascular Parameters
This study presents a typical range for cardiovascular performance parameters in a population of 4–8-year-old children with congenital heart disease tested in a newly developed outdoor running protocol for CPET. (Source: Pediatric Cardiology)
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Autosomal Recessive Long QT Syndrome: Clinical Aspects and Therapy
AbstractThe autosomal recessive (AR) form of Long QT Syndrome (LQTS) is described both associated with deafness known as Jervell and Lange-Nielsen (JLN) syndrome, and without deafness (WD). The aim of the study is to report the characteristics of AR LQTS patients and the efficacy of the therapy. Data of all children with AR LQTS referred to the Bambino Ges ù Children’s Hospital IRCCS from September 2012 to September 2021were included. Three (30%) patients had compound heterozygosity and 7 (70%) had homozygous variants of theKCNQ1 gene, the latter showing deafness. Four patients (40%) presented aborted sudden cardiac dea...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Outcomes and Risk Factors of Interventions for Pediatric Post-operative Pulmonary Vein Stenosis
AbstractPulmonary vein stenosis (PVS) in children is a challenging condition with poor outcomes. Post-operative stenosis can occur after repair of anomalous pulmonary venous return (APVR) or stenosis within native veins. There is limited data on the outcomes of post-operative PVS. Our objective was to review our experience and assess surgical and transcatheter outcomes. Single-center retrospective study was performed including patients  <  18 years who developed restenosis after baseline pulmonary vein surgery that required additional intervention(s) from 1/2005 to 1/2020. Non-invasive imaging, catheterization and ...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Reintervention Before Bidirectional Cavopulmonary Shunt and Intermediate Outcomes in Children with Single Ventricle Who Underwent Main Pulmonary Artery Banding
AbstractUnplanned reinterventions following pulmonary artery banding (PAB) in single ventricle patients are common before stage 2 palliation (S2P) but associated risk factors are unknown. We hypothesized that reintervention is more common when PAB is placed at younger age and with a looser band, reflected by lower PAB pressure gradient. Retrospective single center study of single ventricle patients undergoing PAB between Jan 2000 and Dec 2020. The association with reintervention and successful S2P was modeled using exploratory cause-specific hazard regression. A multivariable model was developed adjusting for clinical and ...
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research

Twin JET Engines: Multiple JET Foci in Patient With Heterotaxy
(Source: Pediatric Cardiology)
Source: Pediatric Cardiology - September 26, 2023 Category: Cardiology Source Type: research