Pulmonary Artery Sarcoma is a Predominantly Bilateral Disease: Insight from a 55 Case Single Center Experience

Pulmonary artery sarcoma (PAS) is an exceedingly rare disease with historically poor survival. PAS is often mistaken for chronic thromboembolic pulmonary hypertension (CTEPH) owing to similarities in clinical presentation. Controversy exists regarding need to definitively differentiate PAS from CTEPH prior to surgical therapy. Furthermore lung resection would seem inferior palliation to tumor endarterectomy in a predominantly bilateral disease dominated by hemodynamic compromise.

Source: The Journal of Heart and Lung Transplantation - March 31, 2020 Category: Transplant Surgery Authors: C.Y. Lee, D.G. Papamatheakis, M.A. Bautista, Y.K. Gernhofer, K.M. Kerr, D.S. Poch, T.M. Fernandes, N.H. Kim, M.M. Madani, V. Pretorius Tags: (55) Source Type: research