Congenital Peritoneal Encapsulation and Nephrotic Syndrome.

We report a case of CPE diagnosed postmortem in a 23-year-old man who suffered severe acute nephrotic syndrome and CT findings of uncertain significance in ileocecal region. The patient was admitted due to abdominal and back pain. In the last days of hospitalization, there were no signs or symptoms; despite this, the patient was found dead in the hospital bed. Postmortem examinations showed signs of diffuse altered abdominal blood supply, especially in bowel and liver, without signs of perforation and/or peritonitis. In the absence of an anatomical obstruction, we found that an intra-abdominal hypertension related to a severe edema of all the loops in the small intestine developed. This process, potentially, could have induced an indirect obstructive mechanism with development of bowel ischemia in the absence of a direct obstruction. Similar cases, in which CPE is associated with nephrotic syndrome, are not reported in literature. PMID: 31986230 [PubMed - as supplied by publisher]
Source: Journal of Forensic Sciences - Category: Forensic Medicine Authors: Tags: J Forensic Sci Source Type: research