Simplified mitral valve repair in pediatric patients with connective tissue disorders

Congenital cardiac surgeons are rarely called upon to correct severe mitral valve regurgitation (MR) in pediatric patients with connective tissue disorders (CTD). Patients in this relatively uncommon diagnostic group will present in childhood with aortic root enlargement, MR, or both. Severe MR is the typical mode of early clinical presentation of patients with infantile Marfan Syndrome (MFS), and can be associated with failure to thrive, pulmonary hypertension, congestive heart failure and ventilator-dependence.
Source: Operative Techniques in Cardiac and Thoracic Surgery - Category: Cardiovascular & Thoracic Surgery Authors: Source Type: research