TGA like physiology

TGA like physiology – cyanotic heart disease with high pulmonary blood flow Following congenital heart diseases have cyanosis with high pulmonary blood flood flow (TGA like physiology or transposition like physiology): Dextro transposition of great arteries (D- TGA) with ventricular septal defect (VSD) and no pulmonary stenosis (PS) Double outlet right ventricle (DORV) with VSD and no PS Tricuspid atresia with VSD and no PS TGA like physiologies can present with cyanosis and heart failure in very early life due to increased pulmonary blood flow as there is no pulmonary stenosis to restrict the pulmonary blood flow. D-TGA with VSD and no PS is a condition which can cause cyanosis on first day of life. This is in contrast to Tetralogy where the onset of cyanosis is delayed. Some of these patients may need pulmonary artery banding to reduce pulmonary blood flow if immediate surgical correction is not feasible. In case of D-TGA early surgical correction with arterial switch operation (Jatene’s operation) is ideal. TGA physiologies do not have hypercyanotic spells (cyanotic spells) and they do not give history of squatting which occurs in later life with TOF (tetralogy of Fallot) like physiologies. The post TGA like physiology appeared first on Cardiophile MD.
Source: Cardiophile MD - Category: Cardiology Authors: Tags: General Cardiology Arterial switch operation cyanotic heart disease cyanotic heart disease with high pulmonary blood flow d-TGA dextro transposition of great arteries DORV Jatene's operation PS Pulmonary stenosis TGA like physiology Source Type: blogs