Clinical Features in Adolescent and Adult Cases with Pulmonary Hypertension Associated with Congenital Portosystemic Shunt

Purpose: Congenital portosystemic shunts (CPSS) are rare vascular malformations which cause partial or complete shunting of portal blood into the systemic circulation. Pulmonary arterial hypertension (PAH) is one of its major complications, and therapeutic outcomes for children have been reported. However, clinical courses of CPSS-related PAH in adolescent and adult cases are not well known.
Source: The Journal of Heart and Lung Transplantation - Category: Transplant Surgery Authors: Source Type: research