Symptoms and quality of life in adults with cystic fibrosis: A cross-sectional analysis of the InSPIRe:CF trial

People living with cystic fibrosis (CF) often report a high symptom burden comprising physical (e.g., cough, dyspnea), psychosocial (e.g., depression, anxiety) and existential (e.g., fear of dying) symptoms [1 –6]. Advances in CF care such as highly effective modulator therapy (HEMT), improved airway clearance therapies, nutritional support, and lung transplantation are projected to add decades to the lives of people with CF, with a median predicted survival of 56 years [7,8]. HEMT refers to a specific combination of drugs effective in correcting the malfunctioning protein made by the CFTR gene [9].
Source: Journal of Cystic Fibrosis - Category: Respiratory Medicine Authors: Tags: Original Article Source Type: research