Acquired myelinated retinal nerve fiber layer in a  child with neurofibromatosis 1–related optic pathway glioma

Myelinated retinal nerve fiber layer (RNFL) is a rare structural anomaly that occurs from abnormal myelination extending anterior to the lamina cribrosa. Clinically, myelinated RNFL is characterized as a gray-white lesion with feathered, well-demarcated borders obscuring the retinal vasculature. Myelinated RNFL is typically congenital, benign, and asymptomatic. It is most commonly noted as an incidental finding on ophthalmic examination. However, cases of acquired myelinated RNFL have been reported.
Source: Journal of AAPOS - Category: Opthalmology Authors: Tags: Short Report Source Type: research