Surgical repair of peripheral pulmonary artery stenosis: A two-decade experience with 145 patients

Peripheral pulmonary artery stenosis (PPAS) is a relatively rare form of congenital heart disease often associated with Williams syndrome, Alagille syndrome, and elastin arteriopathy. This disease is characterized by stenoses at nearly all lobar and segmental ostia and results in systemic level right ventricular pressures. The current study summarizes our experience with the surgical treatment of PPAS.
Source: The Journal of Thoracic and Cardiovascular Surgery - Category: Cardiovascular & Thoracic Surgery Authors: Source Type: research