Postoperative tracheal compression requiring transposition of the brachiocephalic artery after Bentall operation combined with total arch replacement in a patient with Loeys-Dietz syndrome

Loeys –Dietz syndrome (LDS) is an autosomal dominant connective tissue disorder similar to Marfan syndrome (MFS), which mainly consists of vascular lesions (aneurysm and dissection), skeletal abnormalities, head and facial abnormalities, and skin lesions [1, 2]. Compared to MFS, LDS has more severe vasc ular symptoms and lesions are found in a wide range of arteries; hence, surgical interventions for aortic dissection and cerebral hemorrhage are often required from a young age [3]. Despite this, there are only a handful of reports on perioperative management of LDS and points of caution in airway m anagement have yet to be clarified.

Source: Journal of Cardiothoracic and Vascular Anesthesia - July 17, 2021 Category: Anesthesiology Authors: Tsukamoto Marumi, Kondo Takashi, Miyoshi Hirotsugu, Toyota Yukari, Yokomi Hiroshi, Sumii Ayako, Shorin Daiki, Takahashi Shinya, M Tsutsumi Yasuo Tags: CASE REPORT Source Type: research