A case of catecholaminergic polymorphic ventricular tachycardia masquerading as an intractable seizure

Reza Shabanian, Manizheh Ahani, Shima Zandiyeh, Aliyeh Nikdoost, Minoo Dadkhah, Parvin Akbari Asbagh, Reza Shervin BadvAnnals of Pediatric Cardiology 2020 13(2):141-143 A 5-year-old boy with the history of intractable seizure for the past 2 years was transferred to the emergency room for cardiopulmonary resuscitation because of the prolonged seizure and profound cyanosis. He was intubated and resuscitated by cardioversion for a bizarre shape ventricular tachycardia (VT). After noxious stimulation, he showed multiple polymorphic ventricular premature beats that were followed by a bidirectional VT in favor of catecholaminergic polymorphic VT. The genetic assessment was positive for CASQ2 mutation. In the follow–up, the arrhythmia was controlled by nadolol, however with a prominent neurological sequela.
Source: Annals of Pediatric Cardiology - Category: Cardiology Authors: Source Type: research