Pulmonary arterial hypertension in congenital heart disease - Part I

Pneumologie. 2023 Nov;77(11):956-961. doi: 10.1055/a-2146-7434. Epub 2023 Nov 14.ABSTRACTThe number of adults with congenital heart disease (CHD) is steadily rising and amounts to approximately 360,000 in Germany. CHD is often associated with pulmonary arterial hypertension (PAH), which may develop early in untreated CHD. Despite timely treatment of CHD, PAH often persists or recurs in older age and is associated with significant morbidity and mortality.The revised European Society of Cardiology/European Respiratory Society 2022 guidelines for the diagnosis and treatment of PH represent a significant contribution to the optimized care of those affected. However, the topic of "adults with congenital heart defects" is addressed only relatively superficially in these guidelines. Therefore, this article addresses the perspective of congenital cardiology in greater depth.PMID:37963485 | DOI:10.1055/a-2146-7434

Source: Pneumologie - November 14, 2023 Category: Respiratory Medicine Authors: Harald Kaemmerer Gerhard Paul Diller Ingo D ähnert Christina A Eichstaedt Andreas Eicken Annika Freiberger Sebastian Freilinger Ralf Geiger Matthias Gorenflo Ekkehard Gr ünig Alfred Hager Ulrike Herberg Michael Huntgeburth Ann-Sophie Kaemmerer Rainer Ko Source Type: research