A clinical review of congenital hepatic fibrosis diagnosed in adulthood: presentation, complications, and outcomes

CONCLUSIONS: CHF should be considered when patients present with cholangitis and/or complications of portal hypertension and have a cirrhotic appearing liver and renal cysts on imaging. Depending upon the disease severity, interventions such as TIPS or LT may be required.PMID:37802414 | DOI:10.1016/j.aohep.2023.101164

Source: Annals of Hepatology - October 6, 2023 Category: Gastroenterology Authors: Lauren Loeb Jason Lewis Zhongwei Peng Michael G Heckman Raouf Nakhleh Andrew P Keaveny Source Type: research