Immune-mediated Necrotizing Myositis Associated Fulminant Myocarditis Recovered On Peripheral Veno-arterial Extracorporeal Membrane Oxygenation

A 41-year-old male with anti-signal recognition particle (SRP) positive immune-mediated necrotizing myositis (IMNM) on abatacept, prednisone, and subcutaneous immune globulin previously refractory to conventional diseases modifying antirheumatic drugs and biologic agents (intravenous immune globulin, azathioprine, methotrexate, tacrolimus, rituximab) presented for shortness of breath and right sided chest pain. He was found to have new onset atrial flutter with 2:1 conduction. Chest CTA demonstrated multiple right sided segmental pulmonary emboli.
Source: Journal of Cardiac Failure - Category: Cardiology Authors: Tags: 360 Source Type: research