Intravoxel incoherent motion (IVIM) MRI in pediatric patients with synovitis of the knee joint: a prospective pilot study
Diagnosing synovial inflammation by administration of gadolinium-based contrast agents is limited by invasiveness and possible side effects, especially in children and adolescents. (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - November 16, 2022 Category: Rheumatology Authors: Britta Huch, Kilian Stumpf, Anna-Katinka Bracher, Volker Rasche, Daniel Vogele, Catharina Sch ütz, Aleš Janda, Meinrad Beer and Henning Neubauer Tags: Research article Source Type: research

Pulmonary manifestations of childhood-onset primary Sjogren ’s syndrome (SS) masquerading as reactive airways disease in a male patient and review of interstitial lung disease associated with SS
Sjogren ’s syndrome (SS) is a rare chronic autoimmune disease involving exocrine glands presenting with sicca syndrome, recurrent parotitis and other extraglandular stigmata. SS is well characterized in the adu... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - November 16, 2022 Category: Rheumatology Authors: Adam Bartholomeo, Shean Aujla, Meryle Eklund, Cheryl Kerrigan, Ellen Riemer and Mileka Gilbert Tags: Case Report Source Type: research

Juvenile Dermatomyositis: what comes next? Long-term outcomes in childhood myositis from a patient perspective
To describe long-term outcomes in JDM using patient questionnaires and link to longitudinal, prospectively collected data for each patient within the Juvenile Dermatomyositis Cohort and Biomarker Study, UK and... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - November 16, 2022 Category: Rheumatology Authors: C. Boros, L. McCann, S. Simou, D. Cancemi, N. Ambrose, C. A. Pilkington, M. Cortina-Borja and L. R Wedderburn Tags: Research article Source Type: research

Real-world comparison of the effects of etanercept and adalimumab on well-being in non-systemic juvenile idiopathic arthritis: a propensity score matched cohort study
Etanercept (ETN) and adalimumab (ADA) are considered equally effective biologicals in the treatment of arthritis in juvenile idiopathic arthritis (JIA) but no studies have compared their impact on patient-repo... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - November 14, 2022 Category: Rheumatology Authors: Joeri W. van Straalen, Sytze de Roock, Gabriella Giancane, Alessandro Consolaro, Marite Rygg, Ellen B. Nordal, Nadina Rubio-P érez, Marija Jelusic, Jaime De Inocencio, Jelena Vojinovic, Nico M. Wulffraat, Patricia C. J. Bruijning-Verhagen, Nicolino Ruper Tags: Research article Source Type: research

Systemic lupus of pediatric onset in Afro-Caribbean children: a cohort study in the French West Indies and French Guiana
Systemic diseases of pediatric onset are more frequent in the Afro-Caribbean population. We performed a study of patients followed in the French overseas departments of America (FOAD) for pediatric systemic lu... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - November 12, 2022 Category: Rheumatology Authors: Arthur Felix, Frederique Delion, Benoit Suzon, Elise Martin, Anais Ogrizek, M ’hamed Mohamed Sahnoun, Claudia Hospice, Aurelie Armougon, Emma Cuadro, Narcisse Elenga, Moustapha Dramé, Brigitte Bader-Meunier, Christophe Deligny and Yves Hatchuel Tags: Research article Source Type: research

ANCA-associated vasculitis with cardiac valve vegetations in two teenage males: two case reports and a literature review
Anti-neutrophil cytoplasm antibody (ANCA)-associated vasculitis is a term used to describe systemic vasculitides that affect small and medium-sized blood vessels. Granulomatosis with Polyangiitis (GPA), a type... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 28, 2022 Category: Rheumatology Authors: Alexandra Theisen, Carrie L. Phillips and Martha Rodriguez Tags: Case Report Source Type: research

Overlap syndrome in a 12-year-old girl with systemic lupus erythematosus and anti-oj antibody-positive polymyositis: a case report
We present the case of a 12-year-old girl di... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 21, 2022 Category: Rheumatology Authors: Kan-Hsuan Lin and Jun-Kai Kao Tags: Case Report Source Type: research

Longitudinal assessment of preparation for care transition among adolescents and young adults with rheumatologic disease: a single-center pilot study
Adolescents and young adults (AYA) with rheumatologic diseases are at high risk for poor outcomes and gaps in care when transitioning from pediatric to adult care. However, tools for evaluating transition read... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 21, 2022 Category: Rheumatology Authors: Jordan E. Roberts, Olha Halyabar, Carter R. Petty, Maria Alfieri, Brittany Esty, Johnathan Dallas, Melissa Hazen, Sandra Stein and Mary Beth F. Son Tags: Short Report Source Type: research

Pathophysiology, clinical manifestations and current management of IL-1 mediated monogenic systemic autoinflammatory diseases, a literature review
Systemic autoinflammatory diseases (SAIDs) are hyperinflammatory and immune-dysregulation conditions that present in childhood. This kind of disease is a rare disease with early-onset, severe condition and dif... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 17, 2022 Category: Rheumatology Authors: Yandie Li, Meiping Yu and Meiping Lu Tags: Review Source Type: research

Blood transcriptomics to facilitate diagnosis and stratification in pediatric rheumatic diseases – a proof of concept study
This study aims to improve the early diagnosis of pediatric rheumatic diseases by inve... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 17, 2022 Category: Rheumatology Authors: My Kieu Ha, Esther Bartholomeus, Luc Van Os, Julie Dandelooy, Julie Leysen, Olivier Aerts, Vasiliki Siozopoulou, Eline De Smet, Jan Gielen, Khadija Guerti, Michel De Maeseneer, Nele Herregods, Bouchra Lechkar, Ruth Wittoek, Elke Geens, Laura Claes & helli Tags: Research article Source Type: research

Revising the WHO Essential Medicines List for paediatric rheumatology update
(Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 14, 2022 Category: Rheumatology Authors: Waheba Slamang, Nicola Smith, Chris Scott and Helen Foster Tags: Letter to the Editor Source Type: research

Tumor necrosis factor inhibitors for pediatric patients with SAPHO syndrome associated with acne conglobata
Synovitis, acne, pustulosis, hyperostosis, and osteitis (SAPHO) syndrome is a rare chronic inflammatory disease with osteoarticular and cutaneous involvements as its main manifestations. Acne conglobata as a s... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 12, 2022 Category: Rheumatology Authors: Shengyan Liu, Xia Wu, Yihan Cao, Zhaohui Li, Yuchen Liu, Mingwei Ma and Chen Li Tags: Letter to the Editor Source Type: research

Synchronous disease onset and flares in siblings with PFAPA
Periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) is a clinical syndrome of unclear etiology. PFAPA has generally been considered a non-hereditary fever syndrome; however, this ha... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 5, 2022 Category: Rheumatology Authors: Kristen L. Dammeyer, Amanda Schneider, Max M. April and Philip J. Kahn Tags: Case Report Source Type: research

Incomplete penetrance of NOD2 C483W mutation underlining Blau syndrome
Blau syndrome (BS) is a rare autoinflammatory disorder with NOD2 gain-of-function mutation and characterized by autoactivation of the NF κB pathway. Classically considered a disease of high penetrance, reports on (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 3, 2022 Category: Rheumatology Authors: Shao-Yu Chang, Naotomo Kambe, Wen-Lang Fan, Jing-Long Huang, Wen-I Lee and Chao-Yi Wu Tags: Case Report Source Type: research

Transitioning patients with juvenile idiopathic arthritis to adult care: the Nordic experience
In this study, we examined the transferral rates and disease... (Source: Pediatric Rheumatology)
Source: Pediatric Rheumatology - October 1, 2022 Category: Rheumatology Authors: Katriina Mikola, Katariina Rebane, Ellen Dalen Arnstad, Lillemor Berntson, Anders Fasth, Mia Glerup, Troels Herlin, Hannu Kautiainen, Susan Nielsen, Ellen Nordal, Suvi Peltoniemi, Marite Rygg, Veronika Rypdal, Marek Zak and Kristiina Aalto Tags: Research article Source Type: research