Progress of macular atrophy during 30 months ’ follow-up in a patient with spinocerebellar ataxia type1 (SCA1)

ConclusionsThe full-field scotopic and photopic ERGs were normal. The mfERGs were significantly smaller in the central region. OCT demonstrated bilateral photoreceptor atrophy in the macula, and the rate of EZ loss was more rapid than in other macular dystrophies. Spark-like hypoautofluorescence appeared during the course of the disease process which might be a specific feature of SCA1-related retinopathy.
Source: Documenta Ophthalmologica - Category: Opthalmology Source Type: research