Pathobiology of inherited biliary diseases: a roadmap to understand acquired liver diseases

Nature Reviews Gastroenterology & Hepatology, Published online: 05 June 2019; doi:10.1038/s41575-019-0156-4New knowledge has been steadily acquired in genetic and congenital cholangiopathies. Here, the authors discuss Alagille syndrome, polycystic liver diseases, fibropolycystic liver diseases and cystic fibrosis-related liver disease and the insights that these conditions provide into the mechanisms of acquired cholangiopathies.

Source: Nature Reviews Gastroenterology and Hepatology - June 4, 2019 Category: Gastroenterology Authors: Luca Fabris Romina Fiorotto Carlo Spirli Massimiliano Cadamuro Valeria Mariotti Maria J. Perugorria Jesus M. Banales Mario Strazzabosco Source Type: research