A case of coarctation of the abdominal aorta and renal artery stenosis due to neurofibromatosis type 1

We report a case of an adolescent female with history of neurofibromatosis type 1 (NF1) found to have incidental hypertension. She was hypertensive in all four extremities with medical treatment. CT angiogram confirmed narrowing of the abdominal aorta above the bifurcation and atrophic left kidney (figures 1–3). Treatment with a graft to bypass the stenotic segment was performed (figure 4). Figure 1Axial CT with contrast showing superior mesenteric artery (red arrow) enlarged as compared with descending abdominal aorta. Figure 2Coronal CT maximum intensity projection view of narrowed segment of descending abdominal aorta (red arrow). Figure 3T2-weighted axial MRI showing atrophic left kidney (arrow) from the long-standing narrowing of the abdominal aorta by the superior mesenteric artery. Figure 4Postoperative volume rendered image...

Source: Postgraduate Medical Journal - March 22, 2017 Category: Journals (General) Authors: Veean, S., Thakkar, N., Gupta, S., Keshavamurthy, J. Tags: Urology, Journalology, Genetics, Hypertension, Histopathology, Radiology, Clinical diagnostic tests, Urological surgery, Ethics Images in medicine Source Type: research