Teaching NeuroImages: Carotid cavernous fistula in a patient with Ehlers-Danlos syndrome

A 25-year-old woman with Ehlers-Danlos syndrome type IV and history of spontaneous right petrous internal carotid artery dissection presents with severe headache, right eye pain with extraocular movements, proptosis, and chemosis of the right eye. She reported hearing her heartbeat in her right ear. CT angiogram (figure) revealed an engorged right ophthalmic vein. Subsequent digital subtraction angiography confirmed a carotid cavernous fistula along a previously dissected carotid artery.

Source: Neurology - August 28, 2016 Category: Neurology Authors: Liang, J. W., Horowitz, D. Tags: CT, Other cerebrovascular disease/ Stroke, Arteriovenous malformation, Carotid artery dissection RESIDENT AND FELLOW SECTION Source Type: research