Reversal of cylindrical bronchial dilatations in a subset of adults with cystic fibrosis treated with elexacaftor/tezacaftor/ivacaftor
Conclusions
Although bronchial dilatations are generally considered irreversible, ETI was associated with reversal, which was limited to the cylindrical bronchial dilatation subtype, and occurred in a small subset of awCF. Initiating ETI earlier in life may reverse early bronchial dilatations.
Source: European Respiratory Journal - Category: Respiratory Medicine Authors: Cazier, P., Chassagnon, G., Dhote, T., Da Silva, J., Kanaan, R., Honore, I., Carlier, N., Revel, M.-P., Canniff, E., Martin, C., Burgel, P.-R. Tags: CF and non-CF bronchiectasis Original Articles: Cystic fibrosis Source Type: research