Problem diagnostyczny: gorączkujący nastolatek z rzadkim zespołem chorobowym

Publication date: Available online 15 May 2015 Source:Pediatria Polska Author(s): Paweł Małecki , Agnieszka Gałek , Jadwiga Małdyk , Ludomiła Machowska , Katarzyna Jończyk-Potoczna , Katarzyna Derwich Haemophagocytic syndrome (hemophagocytic lymphohistiocytosis, HLH) is a rare hematologic disorder which manifests itself by inflammatory reaction caused by incorrect activation of immune cells. A 16-year-old boy was admitted to the hospital with a high fever, respiratory distress, dyspnea, rash and hepatosplenomegaly. The differential diagnosis initially considered infectious mononucleosis and Kawasaki disease. Eventually the boy was transferred to the Department of Pediatric Oncology, Hematology and Transplantology in Poznań in which, in the course of extensive diagnosis, HLH triggered by HHV-6 infection, was established. Treatment was initiated according to the HLH 2004 protocol. Clinical improvement was achieved.
Source: Pediatria Polska - Category: Pediatrics Source Type: research