Cancer-associated regional ischemic myopathy: a rare myopathy

Paraneoplastic myopathies are often inflammatory or necrotizing, and can be associated with specific antibodies.[1] Regional ischemic immune myopathy (RIIM) is a rare disorder attributed to muscle vasculopathy and considered paraneoplastic.[2] Contrary to dermatomyositis, which is associated with complement mediated muscle microangiopathy, capillary depletion, perifascicular pathology and sometimes muscle ischemia,[3] RIIM is characterized by regional necrosis in border zones between damaged perimysial vessels.
Source: Neuromuscular Disorders - Category: Neurology Authors: Source Type: research