Cleavage ‐resistant RIPK1‐induced autoinflammatory syndrome—A report of three generations with periodic fever and clinical response to colchicine
We present a family with three generations affected by CRIA syndrome. Our index patient (P1), a boy born of a non-consanguineous marriage, developed recurrent episodes of fever after 5  months of age, with variable periodicity. His father (P2) and paternal grandmother also had periodic fever. At 23 months of age, P1 was diagnosed with renal biopsy-proven steroid-responsive nephrotic syndrome. His first visit to our center was at 2 years of age. At presentation, he had failur e to thrive, microcytic hypochromic anemia, and elevated inflammatory markers and interleukin-6 levels. Amyloid A protein was elevated, serum cr...
Source: International Journal of Rheumatic Diseases - July 15, 2023 Category: Rheumatology Authors: Akshaya Chougule, Vaishnavi V. Iyengar, Vijaya Gowri, Prasad Taur, Manisha R. Madkaikar, Minnie Bodhanwala, Mukesh M. Desai Tags: CASE REPORT Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review
Conclusions: The viral form of PAN seems to be individualized as a distinct entity, requiring early, aggressive medication.PMID:37374366 | PMC:PMC10305326 | DOI:10.3390/medicina59061162 (Source: Medicina (Kaunas))
Source: Medicina (Kaunas) - June 28, 2023 Category: Universities & Medical Training Authors: Victoria Pa șa Elena Popa Mihaela Poroch Adriana Cosmescu Agnes Iacinta Bacusca Ana Maria Slanina Alexandr Ceasovschih Alexandra Stoica Antoneta Petroaie Monica Ungureanu Andrei Emilian Popa Raluca Ioana Avram Cristina Bologa Vladimir Poroch Elena Adorat Source Type: research