A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/ β⁺-Thalassaemia Patient
Sickle cell disease (SCD) refers to a group of hereditary disorders associated with clinical manifestations of variable severity. C In particular, Fat Embolism Syndrome, a rare and devastating complication of SCD, may preferentially involve non-homozygous patients and patients with mild disease.
Source: Mediterranean Journal of Hematology and Infectious Diseases - Category: Hematology Authors: Marta Bortolotti, Gianluca Costamagna, Marta Mancarella, Delia Gagliardi, Silvia Lanfranconi, Alessia Marcon, Margherita Migone De Amicis, Nereo Bresolin, Stefania Corti, Giovanna Graziadei Source Type: research