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Management of patients with pulmonary atresia and intact ventricular septum (PAIVS) varies widely depending on anatomic characteristics and institutional preference.1 Patients with right ventricle-dependent coronary circulation2 are managed as single-ventricle patients. For patients without right ventricle-dependent coronary circulation (Fig. 1), we (as many others) have advocated a staged approach with initial establishment of continuity between the right ventricle (RV) and pulmonary artery (PA) (with or without an aortopulmonary shunt) to promote RV growth, followed by an “RV overhaul” to enlarge the ventricular cavity by resecting muscle bundles.
Source: Seminars in Thoracic and Cardiovascular Surgery - Category: Cardiovascular & Thoracic Surgery Authors: Tags: ADULT – Commentary Source Type: research