Primary adenoid cystic carcinoma arising from an ectopic lacrimal gland involving both nasal orbits: a rare clinical entity.

We present a case of ACC that occurred in ectopic lacrimal gland tissue involving the medial region of both orbits. A 74-year-old woman was admitted with a 4-week history of progressive painful proptosis in her left eye. Examination revealed a medium-size bilateral nasal canthal mass. Computed tomography (CT) scan revealed a nasal mass in both orbits with bone erosion. The patient underwent bilateral anterior orbitotomy and incisional biopsy was performed. Histopathology exam revealed an ACC with perineural and bone invasion. She refused orbital exenteration and radiation therapy was initiated.
PMID: 32912017 [PubMed - as supplied by publisher]

Source: Orbit - September 9, 2020 Category: Opthalmology Authors: Nava-Castañeda Á, Kahuam-López N, De La Fuente Díez Y, Velásco Y Levy A, Sánchez-Bonilla FG, Martín F, Garnica-Hayashi L, Rodriguez-Reyes A Tags: Orbit Source Type: research