The dark side of the (half) Moon

A 71-year-old man was referred to Neuro-Ophthalmology for evaluation of reading problems associated to pituitary adenoma. Perimetry showed a right temporal crescent syndrome ( “half moon” syndrome) suggesting left occipital disease. Brain MRI, electroencephalogram and CSF examination (14-3-3 protein) were consistent with a diagnosis of Creutzfeldt-Jakob disease. His neurologic condition rapidly deteriorated with memory problems, myoclonus and apathy followed by death, four months later. This case shows how visual problems may be the first manifestation of this rare prion disease (Heidehain variant of Creutzfeldt-Jakob disease).
Source: Survey of Ophthalmology - Category: Opthalmology Authors: Tags: Clinical challenges Source Type: research