Norwood Procedure for Hypoplastic Left Heart Syndrome

Transcript of video: Hypoplastic Left Heart Syndrome is a very severe form of congenital heart disease, in which, the left ventricle, aorta and mitral and aortic valves are hypoplastic and valves may be atretic as well. It has a very poor survival. Norwood procedure is the first stage palliation for hypoplastic left heart syndrome, and a second stage palliaton, bidirectional Glenn procedure is done, to separate the pulmonary and systemic circulations, and finally, a Fontan procedure, Fontan type of procedure, connecting inferior vena cava also to the pulmonary circulation, is done at a still later, as a third stage. This is diagrammatic representation of hypoplastic left heart syndrome. Left ventricular cavity is hypoplastic, mitral valve is either very small or atretic, same is true of aortic valve, and ascending aorta is hypoplastic. This has a very poor survival and factors which help postnatal survival are the presence of a patent ductus arteriosus, and an atrial septal defect. After birth, PDA can be maintained by using prostaglandin infusion, to get time for surgical procedures. This is diagrammatic representation of Norwood procedure. As the aorta is small in hypoplastic left heart syndrome, proximal portion of the pulmonary artery is taken and along with the valve, it is used to reconstruct the proximal aorta, this region, and it is connected to the right ventricle. Left ventricle is not useful as a systemic pump because it is hypoplastic. So the right ventricle is us...
Source: Cardiophile MD - Category: Cardiology Authors: Tags: General Cardiology Source Type: blogs