Respiratory Aspects of Primary Ciliary Dyskinesia
This review article explores the respiratory aspects of primary ciliary dyskinesia (PCD), a rare, heterogenous, genetic disorder characterized by impaired motile ciliary function. It discusses the clinical diagnosis and management strategies for PCD-related respiratory disease, including chronic sinusitis, otitis media with effusion, recurrent pneumonia, and bronchiectasis. The review emphasizes the need for a multidisciplinary approach to optimize care and clinical trials to improve outcomes in individuals with PCD, highlighting the importance of accurate diagnosis.
Source: Clinics in Chest Medicine - Category: Respiratory Medicine Authors: Wilfredo De Jes ús-Rojas, Adam J. Shapiro, Amelia Shoemark Source Type: research
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