Cystic Fibrosis in the Era of Highly Effective CFTR Modulators

Cystic fibrosis (CF) was described as a clinical entity more than eighty years ago.1 –3 With the development of comprehensive care centers and therapies directed at the signs and symptoms of the disease, survival improved.4 What once was a disease only of children has become a chronic disease of adults for whom the median predicted survival is fifty years of age.5,6 As the natural history of CF has evolved, so has the recognition of previously underdiagnosed populations of people with CF, contributing to its rising prevalence around the world.
Source: Clinics in Chest Medicine - Category: Respiratory Medicine Authors: Tags: Preface Source Type: research