Neonatal Microsurgical Repair of a Congenital Abdominal Aortic Aneurysm with a Cadaveric Graft
We present the case of a female fetus diagnosed with an AAA on routine prenatal ultrasound. A postnatal computed tomography angiogram revealed an infrarenal AAA with a narrow proximal neck. Surgery was performed on day of life 14 using a cadaveric femoral artery graft. The proximal anastomosis was performed under the microscope given the severity of the aortic stenosis and the proximity of the renal arteries. The patient's postoperative course was uneventful and she is developing normally 1 year after surgery. The graft remains permeable, albeit with evidence of proximal and distal stenosis and graft calcification on imagi...
Source: European Journal of Pediatric Surgery Reports - March 3, 2021 Category: Surgery Authors: Le-Nguyen, Annie Joharifard, Shahrzad C ôté, Geneviève Borsuk, Daniel Ghali, Rafik Lallier, Michel Tags: Case Report Source Type: research

Delayed Diagnosis of a Pyloric Web Causing Gastric Outlet Obstruction in a 13-Month-Old Girl
In this report, we report a case of a girl in whom a pyloric web was diagnosed at the age of 13 months. [...] Georg Thieme Verlag KG Rüdigerstraße 14, 70469 Stuttgart, GermanyArticle in Thieme eJournals: Table of contents  |  Abstract  |  open access Full text (Source: European Journal of Pediatric Surgery Reports)
Source: European Journal of Pediatric Surgery Reports - March 3, 2021 Category: Surgery Authors: Elifranji, Mohammed Sankar, Jisha Abdelrasool, Israa Brisseau, Guy Tags: Case Report Source Type: research

Loop Ileostomy in Europe's Tiniest Male Newborn for Meconium-Related Ileus
We report the interdisciplinary management of surgically treated MRI in a newborn with a BW of 273 g. According to the worldwide database held by the University of Iowa, he is registered as the tiniest male newborn in Europe. The boy was born in the 25th gestational week by cesarean section after a triplet pregnancy with twin–twin transfusion syndrome, him being the donor. He had a BW of 273 g, whereas his brothers had a BW of 740 g and 722 g. Cardiopulmonary stabilization and ventilation were successful. He developed MRI unresponsive to medical treatment. On day 14 of life, a minilaparotomy was performed in the ...
Source: European Journal of Pediatric Surgery Reports - March 3, 2021 Category: Surgery Authors: Till, Holger Singer, Georg Castellani, Christoph Urlesberger, Berndt Tags: Case Report Source Type: research

Congenital Anterior Urethrocutaneous Fistula with a Persistent Urethral Groove
We report the case of an 8-month-old boy with CAUF that resembles the embryological urethral groove. On examination, a wide urethral groove was noted to cover the midshaft of the penis with a well formed urethra extending proximally and distally and with a normal glandular anatomy, a wide glandular meatus, and a complete foreskin. The urethral groove was tubularized and covered in layers. Surgery was complicated with early superficial skin dehiscence not affecting the urethral repair.Refashioning of the skin was then performed. A satisfactory aesthetic and functional outcome was observed at 7 years' follow-up. Defining the...
Source: European Journal of Pediatric Surgery Reports - January 29, 2021 Category: Surgery Authors: Mosa, Hazem Garriboli, Massimo Tags: Case Report Source Type: research

Thoracoscopic Repair of Congenital Diaphragmatic Hernia in Preterm Neonate at 1 Kilogram
We report the first successful primary thoracoscopic repair of congenital diaphragmatic hernia (CDH) in a preterm infant born at 28 weeks of gestation weighing 1,043 g. Left-sided CDH was incidentally diagnosed on postnatal chest X-ray on day 1. The neonate subsequently underwent thoracoscopic repair with primary closure of the defect on day 8 weighing 1,150 g. Intraoperative arterial blood gas monitoring including end tidal carbon-dioxide remained within normal range throughout. Postoperative recovery was uneventful. One year neurodevelopmental outcome was normal for age with no CDH recurrence. [...] Georg Thieme Verl...
Source: European Journal of Pediatric Surgery Reports - January 28, 2021 Category: Surgery Authors: Choudhry, Muhammad Rusu, Simona Brooks, Peter Ogundipe, Enitan Chuang, Shu-Ling Tags: Case Report Source Type: research

Advantage of Using 8K Ultra-High-Definition Television System for Kasai Portoenterostomy for Biliary Atresia
We report the case of a 61-day-old girl on whom we performed an exploratory laparotomy and diagnosed type III biliary atresia using intraoperative cholangiography. For the first time, we performed an open KPE using an 8K ultra-high-definition television system. This allowed us to clearly view the porta hepatis and to successfully perform the portoenterostomy. [...] Georg Thieme Verlag KG Rüdigerstraße 14, 70469 Stuttgart, GermanyArticle in Thieme eJournals: Table of contents  |  Abstract  |  open access Full text (Source: European Journal of Pediatric Surgery Reports)
Source: European Journal of Pediatric Surgery Reports - January 27, 2021 Category: Surgery Authors: Miyagi, Hisayuki Ishii, Daisuke Hirasawa, Masatoshi Shonaka, Tatsuya Sumi, Yasuo Azuma, Nobuyoshi Tags: Case Report Source Type: research

Preoperative Embolization Facilitates Segmental Resection of Pulmonary Sequestration in an Infant
We present a novel approach to the treatment of a pulmonary sequestration in a 7-month-old male using preoperative embolization followed by a sublobar pulmonary resection. The embolization clearly demarcated the affected lung intraoperatively, thereby facilitating complete removal of the lesion with a segmental lung resection rather than complete lobectomy. [...] Georg Thieme Verlag KG Rüdigerstraße 14, 70469 Stuttgart, GermanyArticle in Thieme eJournals: Table of contents  |  Abstract  |  open access Full text (Source: European Journal of Pediatric Surgery Reports)
Source: European Journal of Pediatric Surgery Reports - January 27, 2021 Category: Surgery Authors: Prasad, Dilan Pennell, Christopher Arthur, Lindsay Grier Prasad, Rajeev Tags: Case Report Source Type: research

Image of the Month: Enterocolitis Following a Pull-through for Total Colonic Hirschsprung Disease in a 2-Year-Old Boy
We present a case of a 2-year-old boy with total colonic Hirschsprung disease (HD) who underwent an ileostomy as a newborn, and then colectomy and pull-through at 10 months of age. Since then he has presented four times with enterocolitis. The case is presented with a focus on evaluating patients with HD who present with obstructive symptoms following corrective surgery. A key image is presented along with questions formatted as a quiz to guide readers through critically evaluating the case. [...] Georg Thieme Verlag KG Rüdigerstraße 14, 70469 Stuttgart, GermanyArticle in Thieme eJournals: Table of contents  |  Abstr...
Source: European Journal of Pediatric Surgery Reports - January 9, 2021 Category: Surgery Authors: Apte, Anisha McKenna, Elise Levitt, Marc A. Tags: Case Report Source Type: research

A Hirschsprung Pull-through, “with a Twist”
European J Pediatr Surg Rep 2020; 08: e95-e98 DOI: 10.1055/s-0040-1717128Hirschsprung disease is the most common neurocristopathy in children, resulting in the congenital loss of enteric ganglia. Surgery, which involves resecting the aganglionic segment and restoring bowel continuity, usually results in a good outcome; however, some patients suffer from multiple episodes of enterocolitis and other obstructive symptoms. A contrast enema, examination under anesthesia, and rectal biopsy can identify the cause of obstruction in many cases, including a rare explanation, a twist of the pull-through, a case of which we present he...
Source: European Journal of Pediatric Surgery Reports - January 9, 2021 Category: Surgery Authors: Ahmad, Hira Halleran, Devin R. Quintanilla, Raquel Gasior, Alessandra C. Wood, Richard J. Levitt, Marc A. Tags: Case Report Source Type: research

Treatment of Ruptured Giant Omphalocele and Gastroschisis with Liver Herniation using a Wound Retractor as a Novel Approach
We report on two cases treated with staged surgical repair using a wound retractor as a silo. With this technique, the liver and intestines could be reduced into the abdomen with secondary closure of the abdominal cavity within the first 1 to 2 weeks of life. [...] Georg Thieme Verlag KG Rüdigerstraße 14, 70469 Stuttgart, GermanyArticle in Thieme eJournals: Table of contents  |  Abstract  |  open access Full text (Source: European Journal of Pediatric Surgery Reports)
Source: European Journal of Pediatric Surgery Reports - December 15, 2020 Category: Surgery Authors: Nelson, Jana Wachowiak, Robin Siekmeyer, Manuela Knuepfer, Matthias Thome, Ulrich Holger, Stepan Lacher, Martin Tags: Case Report Source Type: research

Sirolimus: A Rescue Drug to Control Complications of Extensive Venous Malformation
In this report, we present a successful case of sirolimus treatment in managing an extensive venous malformation in the pelvis of a 21-month-old boy who presented with life-threatening complications. With a history dating since the day 2 of life, the patient suffered from chronic bleeding due to scrotal skin ulcerations, in addition to recurrent attacks of severe bleeding per rectum necessitating hospital admission and blood transfusion (three attacks since the age of 7 months). Pelvic magnetic resonance image showed the typical findings of extensive venous malformation involving the pelvis, perineum, scrotum, and extendin...
Source: European Journal of Pediatric Surgery Reports - December 15, 2020 Category: Surgery Authors: Abdelbaky, Mohamed Aly Ragab, Iman Ahmed AbouZeid, Amr AbdelHamid Mohammad, Shaimaa Abdelsattar Dahab, Mohamed Moussa Elsherbeny, Mohammed Safaan, Hatem Abdelkader Tags: Case Report Source Type: research

Image of the Month: Decision-Making in Surgery for Late Onset Hirschsprung Disease
We present a case of a 14-year-old boy with chronic distension, poor growth, and chronic constipation. He undergoes anorectal manometry and rectal biopsy, confirming the diagnosis of Hirschsprung disease (HD). The case is presented with a key image and associated questions to prompt discussion on strategies for management and treatment of HD in late-diagnosed children. [...] Georg Thieme Verlag KG Rüdigerstraße 14, 70469 Stuttgart, GermanyArticle in Thieme eJournals: Table of contents  |  Abstract  |  open access Full text (Source: European Journal of Pediatric Surgery Reports)
Source: European Journal of Pediatric Surgery Reports - December 3, 2020 Category: Surgery Authors: Apte, Anisha McKenna, Elise Levitt, Marc A. Tags: Case Report Source Type: research

Image of the Month: High Pressure Distal Colostogram in a Patient with an Anorectal Malformation
We present two male patients that underwent a divided sigmoid colostomy with distal mucus fistula in the neonatal period and at 6 months of age underwent a high pressure distal colostogram. In the discussion, we will give some tricks beyond the known rules: how to correctly interpret a high pressure distal colostogram, how to identify the level of a recto-urinary fistula, and how to accurately plan the surgical approach. [...] Georg Thieme Verlag KG Rüdigerstraße 14, 70469 Stuttgart, GermanyArticle in Thieme eJournals: Table of contents  |  Abstract  |  open access Full text (Source: European Journal of Pediatric Surgery Reports)
Source: European Journal of Pediatric Surgery Reports - November 23, 2020 Category: Surgery Authors: Apte, Anisha Brisighelli, Giulia McKenna, Elise Levitt, Marc A. Tags: Case Report Source Type: research

Image of the Month: How to Select the Ideal Surgical Approach in Male Anorectal Malformation with No Visible Fistula
We present a case of a 6-month-old male infant with an anorectal malformation (ARM) who underwent colostomy as a newborn, and now presents for definitive repair. A colostogram is shown to identify the malformation and to help plan for the ideal surgical approach. The case is presented with a focus on surgical strategies for management of ARM in the male infant, with questions for the readers posed in a quiz format. [...] Georg Thieme Verlag KG Rüdigerstraße 14, 70469 Stuttgart, GermanyArticle in Thieme eJournals: Table of contents  |  Abstract  |  open access Full text (Source: European Journal of Pediatric Surgery Reports)
Source: European Journal of Pediatric Surgery Reports - November 23, 2020 Category: Surgery Authors: Apte, Anisha McKenna, Elise Levitt, Marc A. Tags: Case Report Source Type: research

Laparoscopic Management of Mechanical Small Bowel Obstruction Secondary to Meckel's Diverticulum with a Double Basis. A Rare Anatomic Presentation
European J Pediatr Surg Rep 2020; 08: e59-e61 DOI: 10.1055/s-0040-1713902Meckel's diverticulum (MD) is the most common congenital abnormality of the gastrointestinal tract. Intestinal occlusion due to MD is a commonly observed consequence of intussusception or volvulus. Here, we report a case of an 11-year-old boy who presented to the emergency department with acute abdominal pain, bilious vomiting, and abdominal rebound tenderness. Computed tomography scan concluded a diagnosis of intestinal occlusion with no apparent cause. The patient was submitted to diagnostic laparoscopy, and mechanical occlusion by the permeable Mec...
Source: European Journal of Pediatric Surgery Reports - November 23, 2020 Category: Surgery Authors: Mariani, Aurora Siddiqui, Mohammed Boulard, Nicolas Berrebi, Dominique Bonnard, Arnaud Tags: Case Report Source Type: research