Neuromuscular junction related disorders
Among idiopathic inflammatory myopathies (IIM), brachio-cervical inflammatory myopathy (BCIM) constitutes a rare entity basically characterized by progressive weakness in the proximal regions of the arms and neck, the frequent association with other autoimmune diseases, and peculiar histopathological features at muscle biopsy. A 57-year-old woman presented with a 1-yr history of weight loss (-10kg), cervicalgia, bulbar signs and weakness in upper limbs. Clinical examination showed drop head with cervical muscle atrophy, severe proximal muscle weakness in upper limbs and nasal voice with swallowing disorders.
Source: Neuromuscular Disorders - Category: Neurology Authors: S. Souvannanorath, T. Nordine, T. Gendre, J. Lefaucheur, V. Plante-Bordeneuve, J. Authier Source Type: research