Pulmonary fibrosis in dyskeratosis congenita: a case report with a PRISMA-compliant systematic review
Dyskeratosis congenita (DC) is a rare genetic disorder of poor telomere maintenance. Pulmonary fibrosis (PF) related to DC is rarely reported.
Source: BMC Pulmonary Medicine - Category: Respiratory Medicine Authors: Ping Wang and Zuojun Xu Tags: Case report Source Type: research
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