Pleuroparenchymal fibroelastosis in patients affected by systemic sclerosis: What should the rheumatologist do?

This study reveals that patients with ILD-SSc associated with chest HRCT evidence of PPFE require close and recurrent follow-up with periodic evaluation of lung function parameters, DLCO and chest HRCT. Rheumatologists should be aware of this new radiological finding which is accompanied by a negative prognosis, especially when associated with a progressive course. Patients with this radiological pattern need to be monitored with particular attention.
Source: Medicine - Category: Internal Medicine Tags: Research Article: Observational Study Source Type: research