Hypoplastic Left Heart Syndrome With Right Ventricle Compression.

Hypoplastic Left Heart Syndrome With Right Ventricle Compression.
Ann Thorac Surg. 2015 Jul;100(1):e15-7
Authors: Fuchigami T, Nishioka M, Takahashi K, Akashige T, Nagata N
Abstract
A male neonate presented with the aortic atresia-mitral stenosis (AA-MS) variant of hypoplastic left heart syndrome (HLHS) wherein the suprasystemic left ventricular (LV) pressure and large left ventricle shifted the intraventricular septum. A compressed right ventricle made it difficult to maintain stroke volume. To avoid high right ventricular (RV) volume load and output, we used a 2-stage Norwood-Glenn (NW-G) procedure. Bilateral pulmonary artery banding (bPAB) was performed on day of life (DOL) 4. On DOL 58, we performed percutaneous balloon dilation of the bPAB portion. At age 3 months, the NW-G procedure was performed without peripheral pulmonary hypoplasia. The patient is currently doing well.
PMID: 26140801 [PubMed - in process]

Source: The Annals of Thoracic Surgery - July 1, 2015 Category: Cardiovascular & Thoracic Surgery Authors: Fuchigami T, Nishioka M, Takahashi K, Akashige T, Nagata N Tags: Ann Thorac Surg Source Type: research