Atypical Mayer-Rokitansky-K üster-Hauser Syndrome with Bilateral Inguinal Hernia of Adnexa—Laparoscopic Transabdominal Preperitoneal Repair with Ovarian Plication

Atypical Mayer-Rokitansky-K üster-Hauser syndrome is a müllerian agenesis associated with malformations of kidneys or ovaries, including müllerian aplasia, renal aplasia, and cervicothoracic somite dysplasia [1]. Incidence of Mayer-Rokitansky-Küster-Hauser syndrome with genital inguinal hernia is rare and under-reported [2 ,3]. Nonfusion of müllerian ducts in embryonic life leads to hypermobility of ovary and ligaments predisposing to inguinal hernia [3]. Hernia repair and ovarian plication may be considered because it prevents ovarian torsion and infarction and preserves ovarian function [4].
Source: The Journal of Minimally Invasive Gynecology - Category: OBGYN Authors: Tags: Images in Gynecologic Surgery Source Type: research