IgG4-related disease: not just a matter of IgG4

Rheumatology key messagesIgG4-RD causes fibro-inflammatory lesions that mimic malignancy, histiocytic disorders and autoimmune conditions.Diagnosis relies on compatible clinico-pathological findings while some patients lack high serum and tissue IgG4.IgG4-related and –unrelated cases have similar features, including comparable sensitivity to glucocorticoids and rituximab.
Source: Rheumatology - Category: Rheumatology Source Type: research