Imaging hepatic angiomyolipomas: key features and avoiding errors

Hepatic angiomyolipomas (HAMLs) are rare mesenchymal neoplasms, which have highly variable imaging appearances, often leading to misdiagnosis. They belong to the family of perivascular epithelioid cell neoplasms (PEComas). HAMLs have a wide spectrum of imaging appearances due to variable amounts of smooth muscle cells, adipose tissue, and blood vessels in their makeup. Although typically sporadic, they are also associated with tuberous sclerosis. Sporadic lesions tend to be solitary whilst patients with tuberous sclerosis often have multiple HAMLs invariably accompanied by renal AMLs.

Source: Clinical Radiology - October 30, 2019 Category: Radiology Authors: J. Seow, M. McGill, W. Wang, P. Smith, M. Goodwin Tags: Pictorial Review Source Type: research